Dermatofibrosarcoma Protuberans

Pack, George T.

doi:10.1001/archsurg.1951.01250030397008

Cited by 150 publications

(49 citation statements)

References 6 publications

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“…Trauma has been implicated in the development of DFSP in 10% to 20% of cases (3,5,12). Nevertheless, such an association could be coincidental due to patients focusing their attention on a preexisting lesion; DFSP has been reported to occur on surgical scars, old burn scars, vaccination sites, and tattoos (26)(27)(28)(29). Our findings do not allow us to confirm or exclude this potential association.…”

Section: Discussionmentioning

confidence: 99%

Pediatric Dermatofibrosarcoma Protuberans in Madrid, Spain: Multi‐institutional Outcomes

Valdivielso-Ramos

Torrelo

Campos‐Domínguez

et al. 2014

Pediatric Dermatology

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Little is known about the incidence and management of dermatofibrosarcoma protuberans (DFSP) in children. We conducted a retrospective review of all patients younger than 18 years of age treated for DFSP over a period of 11 years (2000-2011) in Madrid, Spain. The sample consisted of 13 children. The average annual incidence of DFSP in the pediatric population corresponded to 1.02 cases per million person-years (95% confidence interval 0.55, 1.73). Sites of involvement were diverse, with 15.3% of tumors found in acral locations. The median tumor size was 3.5 cm × 3 cm and the median time from apparent onset to diagnosis was 36 months. Histopathologic examination revealed conventional (77.0%), pigmented (15.4%), and myxoid (7.6%) variants. The mitotic index was consistently <5 per 10 high-power fields. All lesions were removed using surgical excision. One patient developed a local recurrence because of initial affected margins; none developed metastases. The median duration of clinical follow-up was 70.5 months. This study estimated the average annual incidence rate of DFSP in a population of patients younger than 18 years and reviewed the experience of several hospitals in the management of this tumor.

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Section: Discussionmentioning

confidence: 99%

Pediatric Dermatofibrosarcoma Protuberans in Madrid, Spain: Multi‐institutional Outcomes

Valdivielso-Ramos

Torrelo

Campos‐Domínguez

et al. 2014

Pediatric Dermatology

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“…The treatment of DFSP of the vulva is surgical wide local excision [13, 15–19]. Usually, the prognosis is excellent, with a survival rate of 91% to 100% in those patients who undergo wide local excision for primary and recurrent tumors.…”

Section: Discussionmentioning

confidence: 99%