Current outcomes of one-stage surgical correction for Berry syndrome

Abstract

One-stage repair of Berry syndrome has achieved acceptable outcomes. Reoperations mainly are related to aortic or RPA stenosis, and the reoperation rate is higher when RPA arterioplasty is performed with an aortic cuff.

Berry syndrome: One stage surgical repair in a neonate

“…This eliminates the risk of postoperative aortic arch stenosis henceforth decreasing the risk of proximal segment dilation and compression of right pulmonary artery and the left main bronchus [9]. The detachment and anastomosis of the right pulmonary artery to main pulmonary artery behind the aorta maintains the geometry of the pulmonary arteries.…”

“…Long-term follow-up is required after surgical correction as stenosis at the site of anastomosis is a potential complication. The stenosis can be relieved adequately by percutaneous balloon angioplasty [9,10].…”

“…The utilization of intra-aortic baffle is associated with obstruction of right pulmonary artery and left ventricular outflow tract. The size and growth potential of the baffle also pose as a problem to be utilized successfully in neonates [9].…”

“…In this case, the aorta has to be transected which is associated with increased risk of bleeding along with difficult anastomosis [9].…”

“…This technique demonstrated easy anterior transfer of pulmonary arteries in neonates. This leads to decreased risk of compression of right pulmonary artery by the aorta and the airway [9]. Park et al in 2008 [10] demonstrated two cases of single stage repairs.…”