Curative Partial Hepatectomy in Unilobar Caroli’s Syndrome - Report of Three Cases with Long-Term Follow-Up

Abstract

Caroli’s syndrome is a rare congenital disorder of the hepatobiliary system. In the majority of the patients, the cystic dilatations involve the whole intrahepatic biliary tree. We present 3 patients in whom ectasia of the bile ducts was confined to the left lobe of the liver. They were treated by partial hepatectomy. Two, 4 and 5 years after the resection the patients are doing very well. Unilobar forms of Caroli’s syndrome, even those associated with complications, are curable by surgery.