Craniofacial polyostotic fibrous dysplasia: a case report and review of the literature

Abdelkarim, Ahmad; Green, Ryan; Startzell, James M.; Preece, John W.

doi:10.1016/j.tripleo.2008.03.023

Cited by 47 publications

(58 citation statements)

References 13 publications

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“…29 The degree of deformation depends on the extent and site of the lesion, the age of the patient, and whether the disease is monostotic or polyostotic. Diffuse polyostotic lesions in large weight-bearing bones are prone to lead to bowing deformities that increase with age and skeletal growth.…”

Section: Natural History and Clinical Presentationmentioning

confidence: 99%

Fibrous dysplasia of bone: a clinicopathologic review

Mohan¹

2011

PLMI

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Fibrous dysplasia of the bones is an uncommon congenital skeletal disorder that is found equally in both genders and is not inherited. Its etiology has been linked to an activating mutation of Gsα and the downstream effects of the resultant increase in cAMP. Fibrous dysplasia is categorized as either monostotic or polyostotic, and may occur as a component of McCune-Albright syndrome or the rare Mazabraud syndrome. Long bones, skull bones, and ribs are the most commonly affected bones. The radiological picture is somewhat variable, including a ground-glass appearance, expansion of the bone, and sclerosis surrounding the lesion. Histologically, fibrous dysplasia shows irregularly-shaped trabeculae of immature, woven bone in a background of variably cellular, loosely arranged fibrous stroma. It may be complicated by pathologic fracture, and rarely by malignant transformation. This review examines interesting issues surrounding the etiology of fibrous dysplasia, its clinical and laboratory manifestations, radiological picture, utility of bone biopsy, gross and microscopic pathology, complications, and its differential diagnostic considerations.

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Section: Natural History and Clinical Presentationmentioning

confidence: 99%

Fibrous dysplasia of bone: a clinicopathologic review

Mohan¹

2011

PLMI

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“…The progression usually stops after adolescence 1 . Some authors report that the progression of the lesions may continue during adulthood, resulting in facial deformity and functional problems 14 .…”

mentioning

confidence: 99%

Prognosis for craniofacial fibrous dysplasia after incomplete resection: age and serum alkaline phosphatase

Park¹,

Cheon²,

Kim³

et al. 2010

International Journal of Oral and Maxillofacial Surgery

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“…Fibrous dysplasia (FD) is a non-neoplastic benign disorder in which normal bone is replaced by fibrous tissue and immature bone 1,8,[12][13][14][15][16][20][21] , which may affect one (monostotic) or more bones (polyostotic) 14,17,20 . FD is frequently found in children and young adults 6,17 , such as in the present case of a female 10-year-old patient.…”

Section: Discussionmentioning

confidence: 99%

“…Other treatment options for FD include the use of bi-phosphates 1,7,11-13 to assist in the decrease of bone resorption and of the risk of fracture and malignant transformation [3][4]8,[12][13][14][16][17]19 .…”

Section: Discussionmentioning

confidence: 99%

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Monostotic fibrous dysplasia: a case report with cone-beam computed tomography findings

Costa

Peyneau

Verner

et al. 2017

RGO, Rev. Gaúch. Odontol.

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Fibrous dysplasia is a benign fibrous-osseous lesion in which normal RESUMOA displasia fibrosa é uma lesão fibro-óssea benigna em que o osso normal é substituído por tecido conjuntivo fibroso e osso imaturo, podendo afetar um único osso (monostótica) ou vários ossos (poliostótica), ocorrendo principalmente em crianças e adultos jovens. Quando presente nos ossos faciais, a maxila é envolvida com mais frequência que a mandíbula, podendo causar assimetria facial, além de complicações odontológicas. Nos exames por imagem a característica principal da displasia fibrosa é a aparência de vidro despolido. A tomografia computadorizada é o método ideal para avaliação dessa lesão e relação com estruturas adjacentes. A radiografia convencional, devido a sobreposição de estruturas anatômicas, torna difícil a delimitação da extensão da lesão. O presente estudo teve como objetivo apresentar o relato de caso de um paciente do sexo feminino, 10 anos de idade, com presença de displasia fibrosa na maxila, objetivando orientar os cirurgiões-dentistas com relação às principais características imaginológicas dessa lesão.Termos de indexação: Tomografia computadorizada de feixe cônico. Displasia fibrosa monostótica. Maxila.

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Craniofacial polyostotic fibrous dysplasia: a case report and review of the literature

Cited by 47 publications

References 13 publications

Fibrous dysplasia of bone: a clinicopathologic review

Fibrous dysplasia of bone: a clinicopathologic review

Prognosis for craniofacial fibrous dysplasia after incomplete resection: age and serum alkaline phosphatase

Monostotic fibrous dysplasia: a case report with cone-beam computed tomography findings

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