Corrugation of the skull in Paget's disease of bone

Abstract

Summary Paget's disease of bone has been known for about 100 years and the usual deformities of bone, e.g. bowed tibia, large head, are well described in medical text books. However, there does not appear to have been a description of corrugation of the skull as a recognized deformity in Paget's disease. Three cases are now described to illustrate this deformity as an unusual but valuable sign in this disease.

Some Unusual Features of Paget’s Disease of Bone

“…I also wish to thank Mr. Morris, medical photographer, Mrs. Sheard, medical librarian and Mrs. Hilton, medical secretary for their assistance. I am grateful to Blackwell Scientific Publications Ltd., Publisher of the Postgraduate Medical Journal for giving me permission to publish extracts from Chakravorty et al (1977).…”

Egill Skallagrímsson: The first case of Van Buchem disease?

“…In Chakrovorty's series of 5,000 admissions in one year, PDB was identified in 80 patients, of whom skull involvement was present in only 16 and palpable corrugations in six. 9 Skull involvement is present in less than 50% of patients with PDB. 10 The maxilla is involved in 17% of cases of PDB of the skull, and enlargement of the forehead is the most conspicuous feature.…”

Neurological Complications of Paget's Disease of Bone

“…Earlier articles by the author 1 , 2 , have dealt with some other aspects of this disease, but this paper deals specifically with the neurological complications of Paget's disease, which is a relatively common condition in people of West European extraction, and amongst whom the incidence is somewhat higher in Britain 3 . According to Smith 4 , approximately 750,000 people in the United Kingdom suffer from this specific disease of old age.…”