Corrected Transposition of the Great Vessels with Ebstein Malformation of the Left Atrioventricular Valve

Dekker, A.; Mehrizi, Ali Abouei; Vengsarkar, Avinash S.

doi:10.1161/01.cir.31.1.119

Cited by 20 publications

(3 citation statements)

References 4 publications

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“…32 Most patients with congenitally corrected transposition of the great arteries have an abnormal systemic tricuspid valve, which fulfills the criteria for Ebstein's anomaly in 15% to 50% of cases. 16,[33][34][35] It is unclear whether the fundamental nature of the anomaly is identical in concordant and discordant atrioventricular connections. 36,37 The morphological right ventricle is rarely dilated in congenitally corrected transposition.…”

Section: Associated Cardiac Malformations In Ebstein's Anomalymentioning

confidence: 99%

Ebstein’s Anomaly

Jost¹,

Connolly²,

Dearani³

et al. 2007

Circulation

452

238

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Section: Associated Cardiac Malformations In Ebstein's Anomalymentioning

confidence: 99%

Ebstein’s Anomaly

Jost¹,

Connolly²,

Dearani³

et al. 2007

Circulation

452

238

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“…Ebstein's anomaly of inverted tricuspid valve has been described in 15% -50% of cases of congenitally corrected transposition of great arteries [51] as in Figure 31. The anterior leaflet of inverted Ebstein's anomaly is usually small, malformed and the atrialized inverted right ventricle is poorly developed, not thinned and rarely dilated [52].…”

Section: Left-sided Ebstein's Anomalymentioning

confidence: 99%

Ebstein's Anomaly—An Overview

Muthiah¹

2018

CRCM

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Aim: To present the various echocardiographic spectrum of Ebstein's malformation in adolescence and adults. Introduction: Ebstein's anomaly has different anatomic and hemodynamic variables with clinical manifestations of cyanosis, right-sided heart failure and arrhythmias. The leaflet tethering and dysplasia, together with dilatation of the tricuspid valve ring, constitute the anatomic cause of tricuspid regurgitation observed in this condition. Case Reports: The spectrum of leaflet tethering from mild to extreme with varying degrees of tricuspid regurgitation were documented by echocardiography in a 16-year-old cyanotic male with Ebstein's anomaly associated with an atrial septal defect and mild low tricuspid regurgitation (TR), 22-year-old acyanotic male with right-sided heart failure due to severe tricuspid regurgitation and an intact atrial septum, 55-year-old asymptomatic female with moderate high tricuspid regurgitation. The extreme form was described as an "atretic" membrane in a 28-year-old cyanotic male and as a "blanket" of leaflet tissue in a 30-year-old cyanotic male. Conclusion: Ebstein's anomaly has to be suspected clinically in presence of cyanosis with a WPW (Wolf-Parkinson-White) or atrioventricular (AV) block pattern of ECG and its management is complex and must be individualized. RV (right ventricular) exclusion procedures are preferred in advanced cases.

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“…Most patients with congenitally corrected transposition of the great arteries have an abnormal systemic TV, which fulfills the criteria for EA in 15-50% of cases. It is unclear whether the fundamental nature of the anomaly is identical in concordant and discordant atrioventricular connections [24][25][26]. The morphological RV is rarely dilated in congenitally corrected transposition.…”

Section: Associated Cardiac Defectsmentioning

confidence: 99%

Ebstein’s Anomaly

Usta¹,

Yıldırım²,

Karaağaç³

et al. 2018

Structural Insufficiency Anomalies in Cardiac Valves

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Ebstein's anomaly (EA), a rare congenital heart disease, results from the failure of delamination of tricuspid valve (TV) leaflets from the endocardium of the right ventricle (RV) and apical displacement, particularly of the septal and posterior leaflets of TV. The most commonly accompanying cardiac malformation is atrial septal defect. Most EA cases are sporadic; familial ones are rare. EA patients may present at any age. Symptoms result from TV regurgitation, RV dysfunction, inadequate left ventricular filling owing to ventricular septal bowing, inadequate pulmonary flow, and arrhythmias. Atrial tachyarrhythmias are the most common late complications. There have been more techniques of tricuspid repair reported in the literature than any other congenital or acquired cardiac lesion.Neonatal operation has a higher risk of mortality than the operations performed beyond infancy. Late survival rate and the quality of life for hospital survivors are excellent.

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Corrected Transposition of the Great Vessels with Ebstein Malformation of the Left Atrioventricular Valve

Cited by 20 publications

References 4 publications

Ebstein’s Anomaly

Ebstein’s Anomaly

Ebstein's Anomaly—An Overview

Ebstein’s Anomaly

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Corrected Transposition of the Great Vessels with Ebstein Malformation of the Left Atrioventricular Valve

Cited by 20 publications

References 4 publications

Ebstein’s Anomaly

Ebstein’s Anomaly

Ebstein&#39;s Anomaly—An Overview

Ebstein’s Anomaly

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Ebstein's Anomaly—An Overview