Coronary bypass in a patient with hemophilia B, or Christmas disease

K, Tourbaf; Bettigole, Richard E.; Zizzi, Joseph A.; Subramanian, S.; Andersen, Murray N.

doi:10.1016/s0022-5223(19)38262-5

Cited by 22 publications

(13 citation statements)

References 33 publications

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“…There are several case reports and case series of percutaneous coronary stent insertion and of cardiac surgery in patients with haemophilia A [8][9][10][11][12][13][14] and haemophilia B [11,[15][16][17][18][19][20][21][22][23][24][25][26][27][28][29][30]. Some of the older reports describe perioperative haemostatic strategies that are now outdated, such as plasmapheresis with fresh frozen plasma replacement [17] and reliance on prothrombin complex concentrate [16,18,21].…”

Section: Discussion and Review Of The Literaturementioning

confidence: 99%

Cardiac surgery in patients with haemophilia B: a case report and review of the literature

et al. 2009

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Cardiac surgery for coronary heart disease, and for calcific and degenerative valvular heart disease, will likely become more frequent with an ageing haemophilia population. Our report describes the successful management of an individual with mild haemophilia B undergoing elective aortic valve replacement using a continuous infusion of recombinant factor IX. Emphasis is placed on the multidisciplinary coordination of care required across three hospital sites to ensure an uncomplicated peri- and postoperative course. We also provide a review of the current literature on cardiac surgery in patients with haemophilia B.

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Section: Discussion and Review Of The Literaturementioning

confidence: 99%

Cardiac surgery in patients with haemophilia B: a case report and review of the literature

et al. 2009

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“…Reference lists of original articles were also reviewed. In addition, an extensive search 25 Chronic viral infections with known atheromatic activity including chronic hepatitis C virus 10,16 and human immunodeficiency virus 9,12 were also reported.…”

Section: Review Of the Literaturementioning

confidence: 99%

“…4,7,9 The first reported cases of PWH A were transfused pre-operatively with fresh frozen plasma (FFP) and/or cryoprecipitate 26 and PWH B with FFP and/or prothrombin complex concentrate (PCC). [23][24][25] Except for factor replacement, other hemostatic agents were rarely used as an adjuvant therapy to control blood loss. During CABG the antifibrinolytics that were given were aminocaproid acid, 9,19,22 aprotinin, 11,21 and trans-4-aminomethylcyclohexanecarboxylic acid (tranexamid acid).…”

Section: Review Of the Literaturementioning

confidence: 99%

“…Forty‐three cases were found in 22 articles and two abstracts of congresses’ announcements (20 case reports, four small case series) from 1978 to 2017 . The patients’ demographic data and hemophilia characteristics are depicted in Table .…”

Section: Review Of the Literaturementioning

confidence: 99%

“…None of the patients had a history of an inhibitor development. The reported risk factors for atherosclerosis and ICD were hypertension, hyperlipidemia or hyperhomocysteinemia, diabetes mellitus, obesity, smoking, and positive family history . Chronic viral infections with known atheromatic activity including chronic hepatitis C virus and human immunodeficiency virus were also reported.…”

Section: Review Of the Literaturementioning

confidence: 99%

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Replacement therapy for coronary artery bypass surgery in patients with hemophilia A and B

Kanellopoulou

Nomikou

2018

J Card Surg

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There are only a few cases of patients with hemophilia A and B who have undergone coronary artery bypass surgery. High levels of replacement therapy with factor concentrate either with bolus or continuous infusion are usually required pre-operatively and during the first post-operative days in order to maintain the coagulation deficient factor levels greater than 80% of normal. Heparinization during cardiopulmonary bypass appears to be safe and intra-operative blood salvage using cell saver techniques reduce the need for transfusions.

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Unusual case of coronary artery disease in a patient with severe hemophilia B

Jim

Lam

2002

American J Hematol

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To the Editor: Anaplastic large cell lymphoma (ALCL) presenting with bone marrow (BM) involvement is not common [1]. We report a child of systemic ALCL whose clinical presentation was more akin to acute leukemia and the initial diagnosis was made on the BM biopsy.A 12-month-old girl presented with marked pallor and fever of 2 months duration. On examination she had hepatosplenomegaly bilateral small cervical and axillary lymphadenopathy. A clinical diagnosis of acute leukemia was suggested. Complete blood count revealed haemoglobin of 8.0g%, leukocyte count of 16´10 9 /cm 2 and platelet count of 82´10 9 /cm 2 . Serum uric acid and calcium were normal, and she was sero-negative for human immunode®ciency virus. Peripheral blood smear revealed normocytic normochromic red cell morphology. Dierential count revealed a shift to the left with 5% myelocytes, 3% metamyelocytes. Blasts were not seen. BM aspirate showed a normocellular marrow with normal hemopoietic cells. Atypical cells were not seen. BM trephine biopsy was normocellular, but showed a focus of large, atypical tumor cells with multilobated, pleomorphic, embryolike nuclei, prominent nucleoli, and moderate to abundant agranular cytoplasm. The tumor cells showed positivity for CD30, CD45, CD45RO (UCHL1), ALK-1 and epithelial membrane antigen. ALK-1 expression was seen both in the cytoplasm and in the nucleus (Fig. 1). Immunostains for cytokeratin, CD68, CD3, CD20, and CD15 were negative (antibodies were procured from DAKO, Denmark). A diagnosis of systemic ALCL was made. Following the BM biopsy, a cervical lymph node (LN) biopsy was performed. The LN revealed involvement of the sinuses and perifollicular regions by cells with similar cytological and immunophenotypic characteristics. The child's general condition rapidly deteriorated and she died within the week.

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Coronary bypass in a patient with hemophilia B, or Christmas disease

Cited by 22 publications

References 33 publications

Cardiac surgery in patients with haemophilia B: a case report and review of the literature

Cardiac surgery in patients with haemophilia B: a case report and review of the literature

Replacement therapy for coronary artery bypass surgery in patients with hemophilia A and B

Unusual case of coronary artery disease in a patient with severe hemophilia B

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