Cor Triatriatum

Abstract

Cor triatriatumis a rare congenital anomaly characterized by an embriologic defect in which the common pulmonary vein fails to connect to the left posterior atrial wall. As a result, the left atrium is divided by a fibromuscular membrane in 2 chambers, the posterosuperior chamber that receives the drainage of the pulmonary veins, and the anteroinferior chamber that continues with the mitral valve. We report on a 45-year-old woman whose diagnosis was made because of exertional dyspnea and paroxistic atrial fibrillation.Echocardiography showed a characteristic linear echodense structure crossing the left atrium ( Figure 1A). Magnetic resonance and right catheterization confirmed the diagnosis of cor triatriatum ( Figure 1B,C,D). The patient underwent surgical correction.

Cor triatriatum sinistrum diagnosed in the adulthood: a systematic review

“…In the present study on adults with CTS, 17.5% of patients were asymptomatic at the time of diagnosis. Adults with CTS most frequently present with dyspnoea on exertion, orthopnoea and palpitations 1 8 18 35–39. CHF-related symptoms were present in 26.9% of patients in this review, which is lower than in previous studies 23 27 28 35.…”