Cor triatriatum associated with severe valvular pulmonary stenosis and patent ductus arteriosus: An unreported constellation

Erkut, Bilgehan; Koçak, Hikmet; Kayğın, Mehmet Ali; Ceviz, Naci

doi:10.1016/j.ijcard.2005.08.015

Cited by 5 publications

(4 citation statements)

References 6 publications

(8 reference statements)

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“…Although the combination of cor triatriatum dexter and pulmonary stenosis was reported in the literature, it was either diagnosed in younger ages or this combination was reported in patients who had received interventions to pulmonary stenosis in the past [6]. Our case was a 19 year old male patient having complaints since childhood and had not received any medical treatment.…”

Section: Discussionmentioning

confidence: 84%

Infective endocarditis in the setting of infundibular–valvular pulmonary stenosis with incomplete cor triatriatum dextrum and patent foramen ovale

Şahı̇n

Bildirici

Kandemir

et al. 2008

International Journal of Cardiology

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Section: Discussionmentioning

confidence: 84%

Infective endocarditis in the setting of infundibular–valvular pulmonary stenosis with incomplete cor triatriatum dextrum and patent foramen ovale

Şahı̇n

Bildirici

Kandemir

et al. 2008

International Journal of Cardiology

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“…It is characterised by the presence of a fibromuscular membrane separating the left atrium into two parts: the lower of the chambers communicates with the pulmonary veins and the upper with the mitral valve containing the left-atrial appendage. Atypical forms are usually associated to other cardiac anomalies, the most frequent being atrial septal defects and the second, anomalous pulmonary vein return, although multiple associated anomalies have been reported [2]. The presence of Cor Triatriatum in adulthood is well documented, though the first observations were done in postmortem studies [3].…”

Section: Discussionmentioning

confidence: 99%

“…Transesophageal echocardiography proves fundamental to confirm diagnosis and exclude associated anomalies [2]. This technique also allows performing a differential diagnosis with supramitral valve ring, where the left-atrial appendage is separated from the mitral valve by the membrane.…”

Section: Discussionmentioning

confidence: 99%

Cor triatriatum sinistrum in an elderly man

Almendro‐Delia

Trujillo-Berraquero

Araji

et al. 2008

International Journal of Cardiology

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“…[1][2][3][4][5][6] Hasta donde conocemos, la asociación de CT y síndrome de hemihipertrofia (SH) congénita no ha sido descrita.…”

Section: Introductionunclassified

Síndrome de Silver-Russell (hemihipertrofia) y cor triatriatum en un neonato

Ríos-Méndez

Montero-Monar²,

Fernández-Alvarado³

et al. 2015

arch Argent Pediat

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Presentación de casos clínicos RESUMENTanto el síndrome de hemihipertrofia como el cor triatriatum son patologías sumamente infrecuentes. La hemihipertrofia se define como el sobrecrecimiento completo o parcial de uno de los hemicuerpos. El cor triatriatum es una cardiopatía congénita caracterizada por una membrana que divide la aurícula izquierda en dos cámaras; si esta membrana tiene un orificio restrictivo, provoca obstrucción al pasaje sanguíneo desde las venas pulmonares hacia el ventrículo izquierdo, lo que genera hipertensión y edema pulmonar. En este contexto, el ductus arterioso permeable puede actuar como vía de descompresión del circuito pulmonar al permitir el pasaje sanguíneo desde la arteria pulmonar hacia la aorta. Presentamos a un paciente con diagnóstico de síndrome de Silver-Rusell (hemihipertrofia), cor triatriatum y ductus arterioso con flujo invertido. Hasta donde conocemos, esta asociación de patologías infrecuentes y forma de presentación no se han descrito anteriormente. Palabras clave: corazón triatrial, conducto arterial, hipertensión pulmonar, trastornos del crecimiento, síndrome de Silver-Russell. ABSTRACTHemihypertrophy syndrome and cor triatriatum are extremely rare pathologies. Hemihypertrophy is defined as complete or partial overgrowth of one of the hemibodies. Cor triatriatum is a congenital heart disease characterized by a membrane which separates the left atrium into two chambers; if that membrane has a restrictive hole, it causes obstruction to blood passage from the pulmonary veins into the left ventricle causing hypertension and pulmonary edema. In this context, the patent ductus arteriosus can act as a means of decompression of the pulmonary circuit, because it allows the blood passage from the pulmonary artery to the aorta. We report a patient with Silver-Rusell syndrome (hemihypertrophy), cor triatriatum and ductus arteriosus with reverse flow. To our knowledge, this association of rare pathologies and this clinical presentation have not been described previously. El cor triatriatum (CT) es una cardiopatía congénita acianótica poco frecuente, en la que la aurícula izquierda (AI) está dividida en una cámara posterior o accesoria, que recibe las venas pulmonares, y una cámara anterior o AI verdadera, que está en relación con la válvula mitral y la orejuela. Los signos y síntomas más frecuentes que se presentan en esta patología son soplo, disnea, infecciones respiratorias, insuficiencia cardíaca, hipertensión pulmonar y edema agudo pulmonar. Los últimos son secundarios a la obstrucción del flujo sanguíneo venoso pulmonar hacia la AI verdadera si el orificio de la membrana intraatrial es muy pequeño. Sin embargo, si el orificio no es restrictivo o se presenta asociado a un defecto amplio del septum interatrial en la cámara accesoria, los signos de obstrucción sanguínea pulmonar no se hacen evidentes.Se han comunicado algunos defectos asociados al CT, tales como comunicación interventricular, estenosis de la arteria pulmonar, conexión anómala de las venas pulmonares, persist...

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Cor triatriatum associated with severe valvular pulmonary stenosis and patent ductus arteriosus: An unreported constellation

Cited by 5 publications

References 6 publications

Infective endocarditis in the setting of infundibular–valvular pulmonary stenosis with incomplete cor triatriatum dextrum and patent foramen ovale

Infective endocarditis in the setting of infundibular–valvular pulmonary stenosis with incomplete cor triatriatum dextrum and patent foramen ovale

Cor triatriatum sinistrum in an elderly man

Síndrome de Silver-Russell (hemihipertrofia) y cor triatriatum en un neonato

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