Contrast-enhanced ct and angiographic findings in hepatic perivascular epithelioid cell tumor

Tay, Shee Yen; Lao, Wilson T.; Chen, Ch L.; Chan, Wing P.

doi:10.5334/jbr-btr.428

Cited by 6 publications

(2 citation statements)

References 7 publications

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“…Among 105 patients reported in the literature, 12 patients had hepatitis B virus (HBV), and two had hepatitis C virus infection (Table 2). 1,6,12,16–46 Few patients were found to have HEAML complicated with HBV. However, hepatitis B-positive patients with HCC are quite common, so the diagnosis and treatment of patients requires care to avoid misdiagnosis.…”

Section: Discussionmentioning

confidence: 99%

Hepatic epithelioid angiomyolipoma is scattered and unsuitable for surgery: a case report

Cai

Sun²,

Deng

et al. 2023

J Int Med Res

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Hepatic epithelioid angiomyolipoma (HEAML) is a rare tumour of mesenchymal tissue with a malignant tendency. Occurring most frequently in women, the relative incidence in men and women, according to incomplete statistics, is approximately 1:5. In rare cases, disease occurrence and development is hidden. Lesions are generally discovered as chance findings by patients; abdominal pain is the first symptom, and imaging has no specificity in diagnosing the disease. Therefore, great difficulties exist in the diagnosis and treatment of HEAML. Here, the case of a 51-year-old female patient with a history of hepatitis B, and abdominal pain over 8 months as the initial symptom, is described. The patient was found to have multiple intrahepatic angiomyolipoma. Due to the small and scattered foci, complete resection was impossible, and because of her history of hepatitis B, conservative treatment was undertaken, with the patient undergoing regular follow-up. When hepatic cell carcinoma could not be excluded, the patient was treated with transcatheter arterial chemoembolization. No tumour neogenesis or metastasis was detected at the 1-year follow-up.

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Section: Discussionmentioning

confidence: 99%

Hepatic epithelioid angiomyolipoma is scattered and unsuitable for surgery: a case report

Cai

Sun²,

Deng

et al. 2023

J Int Med Res

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“…The following are available online at , Table S1: Published cases of primary liver PEComas. References [ 27 , 28 , 29 , 30 , 31 , 32 , 33 , 34 , 35 , 36 , 37 , 38 , 39 , 40 , 41 , 42 , 43 , 44 , 45 , 46 , 47 , 48 , 49 , 50 , 51 , 52 , 53 , 54 , 55 , 56 , 57 , 58 , 59 , 60 , 61 , 62 , 63 , 64 , 65 , 66 , 67 , 68 , 69 , 70 , 71 , 72 , 73 , 74 , 75 , 76 , 77 , 78 , 79 , ...…”

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Primary Liver Perivascular Epithelioid Cell Tumor (PEComa): Case Report and Literature Review

Kvietkauskas,

Samuolyte,

Rackauskas

et al. 2024

Medicina

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A primary liver perivascular epithelioid cell tumor (PEComa) is an extremely rare entity. In this article, we present a case report with a review of the literature on the patients diagnosed with primary liver PEComa and an elaboration of diagnostic and treatment modalities. A systematic literature search was conducted using the terms “perivascular epithelioid cell tumor”, “PEComa”, “liver”, and “hepatic”. All articles describing patients diagnosed with primary liver PEComa were included. We identified a total of 224 patients of primary liver PEComa from 75 articles and a case from the present study with a significant preponderance of females (ratio 4:1) and with a mean age of 45.3 ± 12.1 years. Most of the patients (114 out of 224, 50.9%) were asymptomatic. A total of 183 (81.3%) patients underwent surgical hepatic resection at the time of diagnosis, while 19 (8.4%) underwent surveillance. Recurrence and metastases were detected in seven (3.1%) and six (2.7%) patients, respectively. In conclusion, surgical resection remains the cornerstone of therapy; however, the presence of nonspecific imaging features makes it difficult to reach a definite diagnosis preoperatively. Therefore, a multidisciplinary approach should be the gold standard in selecting the treatment modality.

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Hepatic perivascular epithelioid cell tumor

et al. 2016

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Rational:Perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal neoplasm which expresses both myogenic and melanocytic markers. PEComas are found in a variety locations in the body, but up to now only approximately 30 cases about hepatic perivascular epithelioid cell tumor are reported in English language worldwide.Patient concerns:A 32-year-old woman was admitted in our hospital with intermittent right upper quadrant pain for 1 month and recent (1 day) progressive deterioration.Diagnoses:Based on the results of the laboratory examinations and the findings of the computed tomography, the diagnosis of hepatic hamartoma or the hepatocecullar carcinoma with hemorrhage was made.Interventions:The patient underwent a segmentectomy of the liver, and the finally diagnosis of hepatic PEComa was made with immunohistochemical confirmation with HMB-45 and SMA.Outcomes:There is no clinical or radiographic evidence of recurrence 9 months after surgery.Lessons:This kind of tumor is extremely rare and the natural history of PEComa is uncertain, as the treatment protocol for hepatic PEComa has not reached a consensus. But the main treatment of the disease may be surgical resection. Only after long term follow-up can we know whether the tumor is benign or malignant. It appears that longer clinical follow-up is necessary in all patients with hepatic PEComas.

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Contrast-enhanced ct and angiographic findings in hepatic perivascular epithelioid cell tumor

Cited by 6 publications

References 7 publications

Hepatic epithelioid angiomyolipoma is scattered and unsuitable for surgery: a case report

Hepatic epithelioid angiomyolipoma is scattered and unsuitable for surgery: a case report

Primary Liver Perivascular Epithelioid Cell Tumor (PEComa): Case Report and Literature Review

Hepatic perivascular epithelioid cell tumor

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