Congenitally Corrected Transposition of the Great Arteries with Severely Stenotic Bicuspid Aortic Valve in an Adult: A Case Report

Pino, Paolo Giuseppe; Pergolini, Amedeo; Zampi, Giordano; Calicchia, Angela; Chialastri, Claudia; Orsini, Francesca Moschella; Fini, F.; Buffa, Vitaliano; Minardi, Fabiana

doi:10.1111/j.1540-8175.2011.01522.x

Cited by 5 publications

(4 citation statements)

References 10 publications

(11 reference statements)

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“…A case report of a patient with bicuspid aortic valve who developed AS in the fifth decade of life is consistent with this observation. 8 Second, consideration should be given to epicardial systemic lead placement in all adult patients with ccTGA undergoing open heart surgery. The risk of complete heart block is high, and endovascular systemic lead placement is known to present technical challenges.…”

Section: Discussionmentioning

confidence: 99%

Severe Symptomatic Aortic Stenosis in an Octogenarian with Congenitally Corrected Transposition of the Great Arteries

Dewaswala,

Bolanos,

Bhopalwala

et al. 2024

CASE

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Section: Discussionmentioning

confidence: 99%

Severe Symptomatic Aortic Stenosis in an Octogenarian with Congenitally Corrected Transposition of the Great Arteries

Dewaswala,

Bolanos,

Bhopalwala

et al. 2024

CASE

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“…Fricke et al [11][12][13][14] reported that up to 2% of transposition repair patients need an AVR or SAV, which is not a negligible proportion. Native AoV stenosis with congenitally corrected transposition is rare, described only in case reports [26,27].…”

Section: Transposition Type Complex Congenital Heart Diseasementioning

confidence: 99%

Outcomes following aortic valve procedures in 201 complex congenital heart disease cases—results from the UK National Audit

Dorobantu

Visan

Tulloh

et al. 2020

Interactive CardioVascular and Thoracic Surgery

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OBJECTIVES Some patients with complex congenital heart disease (cCHD) also require aortic valve (AoV) procedures. These cases are considered high risk but their outcome has not been well characterized. We aim to describe these scenarios in the current practice, and provide outcome data for counselling and decision-making. METHODS This was a retrospective study using the UK National Congenital Heart Disease Audit data on cCHD patients undergoing aortic valve replacement, balloon dilation (balloon aortic valvuloplasty) or surgical repair (surgical aortic valve repair) between 2000 and 2012. Coarsened exact matching was used to pair cCHD with patients undergoing AoV procedures for isolated valve disease. RESULTS A total of 201 patients with a varied spectrum of cCHD undergoing 242 procedures were included, median age 9.4 years (1 day–65 years). Procedure types were: balloon aortic valvuloplasty (n = 31, 13%), surgical aortic valve repair (n = 57, 24%) and aortic valve replacement (n = 154, 63%). Mortality at 30 days was higher in neonates (21.8% vs 5.3%, P = 0.02). Survival at 10 years was 83.1%, freedom from aortic valve replacement 83.8% and freedom from balloon aortic valvuloplasty/surgical aortic valve repair 86.3%. Neonatal age (P < 0.001), single ventricle (P = 0.08), concomitant Fontan/Glenn (P = 0.002) or aortic arch procedures (0.02) were associated with higher mortality. cCHD patients had lower survival at 30 days (93% vs 100%, P = 0.003) and at 10 years (86.4% vs 96.1%, P = 0.005) compared to matched isolated AoV disease patients. CONCLUSIONS AoV procedures in cCHD can be performed with good results outside infancy, but with higher mortality than in isolated AoV disease. Neonates and patients with single ventricle defects, especially those undergoing concomitant Fontan/Glenn, have worse outcomes.

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“…Association of bicuspid aortic valve with ccTGA is extremely rare (limited to three prior case reports). [1][2][3] Out of the three reports in the literature, aortic stenosis was present in two patients and regurgitation in one patient. This aortic valve morphology, when present, may require surgical management depending upon the severity of valve stenosis/regurgitation and degree of right ventricular dysfunction.…”

mentioning

confidence: 99%

Bicuspid aortic valve and anomalous origin of the right ventricular branch in a patient with congenitally corrected transposition of great arteries: A rare association

Ojha

Malhi

Nagulakonda

et al. 2022

Journal of Cardiac Surgery

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Congenitally Corrected Transposition of the Great Arteries with Severely Stenotic Bicuspid Aortic Valve in an Adult: A Case Report

Cited by 5 publications

References 10 publications

Severe Symptomatic Aortic Stenosis in an Octogenarian with Congenitally Corrected Transposition of the Great Arteries

Severe Symptomatic Aortic Stenosis in an Octogenarian with Congenitally Corrected Transposition of the Great Arteries

Outcomes following aortic valve procedures in 201 complex congenital heart disease cases—results from the UK National Audit

Bicuspid aortic valve and anomalous origin of the right ventricular branch in a patient with congenitally corrected transposition of great arteries: A rare association

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