Congenital Unilateral Facial Palsy and Internal Auditory Canal Stenosis

Lin, Kuo-Jen; Huang, Chao; Leung, Joseph Hang

doi:10.1016/j.pediatrneurol.2008.04.002

Cited by 11 publications

(18 citation statements)

References 12 publications

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“…Congenital IAC stenosis/atresia has also been associated with unilateral facial nerve palsy and hearing loss due to both vestibulocochlear and facial nerve hypoplasia [7]. However, our patient does not have IAC stenosis (normal IAC diameter 4-8 mm) [8] although it is common among patients with cochlear nerve deficiency [9].…”

Section: Discussionmentioning

confidence: 58%

Congenital bilateral facial nerve hypoplasia with sensorineural hearing loss: A case report

Hamizan¹,

Kew²,

Abdullah³

2012

International Journal of Pediatric Otorhinolaryngology

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Section: Discussionmentioning

confidence: 58%

Congenital bilateral facial nerve hypoplasia with sensorineural hearing loss: A case report

Hamizan¹,

Kew²,

Abdullah³

2012

International Journal of Pediatric Otorhinolaryngology

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“…According to a review of the literature, there are rare cases of hypoplasia in both the facial and vestibulocochlear nerves that may have been due to different embryological origins, but only a few have been reported in this case series 3,4,6) . Therefore, we should consider a variety causes including genetic problems or trauma, even though the mother had no specific history of trauma.…”

Section: Discussionmentioning

confidence: 87%

“…Acquired type of CFP could have infec tious, trau matic, iatrogenic, neoplastic, and idiopathic causes 1) . And there is a 90% chance of spontaneous recovery, but the developmental type occurs indepen dently or as part of a recognized syndrome such as Möbius, Poland, Goldenhar, CHARGE, or velocardiofacial syndrome 3,4) . Differential diagnosis of CFP is man datory, be cause it will affect the optimal treatment and prognosis.…”

Section: Introductionmentioning

confidence: 99%

“…There is a documented association between CFP and sensorineural hearing loss (SNHL) 5) , and approximately 23% of patients with congenital SNHL have comorbid internal auditory canal (IAC) stenosis 6) . However, almost patients with congenital SNHL have normal facial nerve, and these patients rarely exhibit functional impairments in both facial and vestibulocochlear nerves 3,4,6) .…”

Section: Introductionmentioning

confidence: 99%

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Monozygotic Twin Cases of Unilateral Sensorineural Hearing loss : Elderly One Accompanied with Internal Auditory Canal Stenosis and Facial Paralysis

서규현¹,

손수민²,

김세윤³

2016

journalofthekoreanchildneurologysociety

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We introduce the case of monozygotic twins with sensorineural hearing loss (SNHL). And one of them had congenital facial paralysis (CFP) accompanied by SNHL and internal auditory canal (IAC) stenosis. Most cases of IAC stenosis are accompanied by SNHL, but the patients in our cases showed CFP also. We confirmed the agenesis of facial and vestibulococchlear nerves with the T2-weighted constructive interference in steady-state magnetic resonance imaging (CISS MRI) scans. We should consider a variety causes including genetic problems or trauma. Although the mother did not have a specific trauma history, she may have prolonged exposure to traumatic events during the first trimester of pregnancy. Clinicians who examine the SNHL, should pay attention to the history, physical and neurologic examination, and audiologic and imaging findings in a patient with or without facial nerve paralysis

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“…In one 5-year-old patient who presented with unilateral facial palsy that had been evident from birth, neuroimages taken when she was 5 years old documented a hearing impairment and trigeminal nerve involvement. 3 The facial palsy in most congenital unilateral facial palsies manifests as either a moderately severe (a score of IV) or a severe (a score of V) dysfunction, according to the House and Brackmann 11 facial nerve grading system. Our patient had a score of V.…”

Section: Discussionmentioning

confidence: 99%

Rapidly Declining Unilateral Hearing Within 1 Month in a Newborn With Internal Auditory Canal Stenosis and Facial Palsy

Lee

Tsao

et al. 2009

J Child Neurol

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Most newborns with congenital unilateral facial palsy are expected to recover; however, when a patient has hearing loss, underlying developmental ear structure abnormalities should be investigated, particularly when the patient has internal auditory canal stenosis, which is rarely reported in newborns. All cases of internal auditory canal stenosis are accompanied by concomitant unilateral or bilateral hearing loss, but none with progressive hearing loss has been reported. We present the case of a newborn with rapidly declining hearing in the left ear within 1 month after birth. The hearing decline was associated with unilateral facial palsy. Using high-resolution computed tomography (CT) of the temporal bone, we diagnosed the patient with congenital internal auditory canal stenosis. This is the first case detected with progressive hearing loss after birth, which implies that prompt diagnosis and early habilitation are warranted, even when the hearing loss is initially mild.

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Congenital Unilateral Facial Palsy and Internal Auditory Canal Stenosis

Cited by 11 publications

References 12 publications

Congenital bilateral facial nerve hypoplasia with sensorineural hearing loss: A case report

Congenital bilateral facial nerve hypoplasia with sensorineural hearing loss: A case report

Monozygotic Twin Cases of Unilateral Sensorineural Hearing loss : Elderly One Accompanied with Internal Auditory Canal Stenosis and Facial Paralysis

Rapidly Declining Unilateral Hearing Within 1 Month in a Newborn With Internal Auditory Canal Stenosis and Facial Palsy

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