Congenital stenosis of the abdominal aorta

Maycock, W. d‘A.

doi:10.1016/s0002-8703(37)91084-6

Cited by 105 publications

(33 citation statements)

References 6 publications

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“…The pathogenesis of idiopathic MAS is speculative and is variously attributed to: failure of the two dorsal aortas to fuse during embryological development [19]; rubella infection [20]; abnormal migration of the kidney, as evidenced by the high incidence of multiple renal arteries (70% in one series) [3].…”

Section: Discussionmentioning

confidence: 99%

Idiopathic mid-aortic syndrome in children

et al. 2008

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Mid-aortic syndrome (MAS) is an uncommon condition characterized by narrowing of the abdominal aorta and stenosis of its major branches. Our goal was to illustrate the presentation, diagnosis and management of six new cases of idiopathic MAS together with 96 cases of idiopathic MAS from the literature. The mean age of the 102 cases was 14.3 years (19 days to 49 years). Our patient who presented at 19 days of age is the youngest reported to date. Clinical presentations included hypertension (94%), claudication (17%), renal failure (4%) and intestinal ischemia (1%). Angiography was the diagnostic imaging study of choice. Renal arteries were involved in 91% of patients, while the superior mesenteric artery and celiac artery were involved in 35%. Thirteen percent of cases were managed medically, and the remainder was treated surgically. Our experience shows that initial conservative blood pressure management of idiopathic MAS is feasible unless medical control of hypertension is unsatisfactory, renal function is at risk or there are symptoms of claudication or intestinal ischemia. Careful timing and planning of a surgical intervention is possible for most cases and may, in select cases, be considered after completion of puberty to allow growth to be completed.

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Section: Discussionmentioning

confidence: 99%

Idiopathic mid-aortic syndrome in children

et al. 2008

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“…Maycock szerint congenitalis malformatio okozhatja, amelynek hátterében a primitív embrionális kettős dorsalis aorta inkomplett fúziója állhat. A fúzió elmaradása igen ritkán kettős hypoplasticus aorta megmaradását okozhatja [12]. Hasonló morfológiai elváltozásokat okozhat a Takayasu-arteritis, főként ázsiai populációban fordul elő [11,13].…”

Section: Megbeszélésunclassified

Atípusos aortacoarctatiók sebészi kezelésének hosszú távú eredményei

Dzsinich¹,

Entz

Berek³

et al. 2016

Orvosi Hetilap

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Bevezetés: Az aortacoarctatio a leggyakoribb congenitalis cardiovascularis elváltozások egyike, azok 5-8%-ában fordul elő. Típusos előfordulási helye az isthmicus szakasz. Atípusos helyen kialakuló coarctatio az esetek mintegy 1%-ában fordul elő és többnyire súlyos hypertoniával szövődik. Célkitűzés: A szerzők célul tűzték ki a kórkép sebészi kezelési lehetőségeinek és azok hosszú távú eredményeinek ismertetését 27 beteg műtéti kezelésével szerzett tapasztalataik alapján. Módszer: A 35 évet felölelő utánkövetés során a diagnosztika és a kezelési módszerek változtak. Napjainkban a morfológiai diagnózis legáltalánosabb módszerei a komputertomográfiás angiográfia és a mágneses rezonanciás angiográfia. Az aortarekonstrukció lehetőségei az endovascularis technikák bevezetésével gazdagodtak, de atípusos aortacoartatio esetében a szerzők ma is túlnyomóan változatos sebészi megoldásokat alkalmaznak. Eredmények: A műtétek után nem veszítettek el beteget. A hypertonia minden esetben jelentősen csökkent. Gyermekkorban operált esetekben a növekedés okozta testméretváltozások 3 esetben újabb rekonstrukciós műtétet indokoltak. Következ-tetések: Az atípusos aortacoarctatio individuális sebészi módszerekkel eredményesen kezelhető. Gyermekkorban operált esetekben a testméret-növekedés a rekonstruált aortaszakasz revízióját teheti szükségessé. Orv. Hetil., 2016, 157(26), 1043-1051. Kulcsszavak: atípusos aortacoarctatio, sebészi kezelés, késői eredmények Surgical treatment of atypical aortic coarctation. Long-term resultsIntroduction: Aortic coarctation is a frequent congenital cardiovascular disorder representing 5-8% of all cases. It is typically localized in the isthmic region. However, in about 1% of cases coarctation may develop in atypical sites of the aorta and it is frequently complicated with severe hypertension. Aim: The aim of the authors was to present diagnostic and surgical methods used in 27 patients with atypical aortic coarctation during the last 35 years with special interest on long-term results. Method: There was a great advance in diagnostic and surgical treatment methods during the time period analyzed in this study. Nowadays morphologic diagnosis is most commonly obtained using computed tomography angiography and magnetic resonance angiography. Some cases were treated with endovascular techniques, but the authors used also a wide variety of surgical approaches in these patients with atypical aortic coarctation. Results: No patient died after surgery and hypertension was reduced in all patients, too. Reintervention was necessary in patients operated in childhood due to change of body measures. Conclusions: Atypical aortic coarctation can be treated surgically with good early and late outcomes. Somatic growth of children may indicate surgical revision.

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“…Controversial theories about it have been proposed. M a y c o c .k [35], for example, suggested two possible causes: 1. the failure o f the dorsal aortas to fuse equally at one point with consequent obliteration or loss of one o f them: 2. kinking of the fused aortas.…”

Section: Etiologymentioning

confidence: 99%

“…Only 10 autopsy cases were reported during this period [1,6,7,24,35,39,44,46,50,57] and its autopsy incidence could be esti mated to be in the order of 1 : 62.500. With the advent of the angio graphic diagnosis [Bahnson et al, 1949], 116 additional cases have been published in the last 20 years [2-5, 8-23, 25-34, 36-38, 41-43, 45, 47-49, 51-56, 58, 59].…”

mentioning

confidence: 92%