Congenital onychodysplasia of the ring finger presenting as a bifid nail

Abstract

Congenital onychodysplasia, or Iso-Kikuchi syndrome, is classically defined as a congenital nail abnormality of one or both index fingers that is often associated with a bone abnormality in the affected finger. We report an unusual case of a 6-year-old girl who presented with an S-shaped, bifid nail of the left ring finger that had been present since birth. X-ray findings were used to confirm a diagnosis of congenital onychodysplasia of the ring finger.

Iso-Kikuchi Syndrome in A Newborn and His Mother

“…Anomalies include: polyonychiawhere there are two small incomplete nails on one finger with the lateral one being larger than its counterpart-, micronychiawhere a small nail is seen in the lateral aspect of the finger, anonychia -meaning the total absence of the nail-, hemionychogryphosis, alterations of the lunula [2] and misalignment [1,4,5,7,[9][10][11].…”

“…However, if symptoms persist, a partial matricectomy of the curved portion of the nail is suggested. [10].…”