Congenital nasal dermoids in children

Abstract

The case of a 27 month old male with a congenital midline nasal dermoid cyst is presented. The child attended the Ear, Nose and Throat outpatient's department in July 1995, with an external midline nasal swelling, which had been present at birth and was noted to be gradually increasing in size. Magnetic resonance imaging (MRI) showed a central defect of the nasal bones, with a soft tissue mass at the upper part of the nasal bridge expanding the nasal septum. There was no radiological evidence of intracranial extension. The child had the nasal mass removed under general anesthesia, through an external rhinoplasty incision. Histopathology confirmed that the mass was a fully excised nasal dermoid cyst. Current investigation and management of this condition is discussed.

Intracranial Dysontogenetic Tumors In Children: Topographic-Histologic Correlations, Own Experience And Review Of The Literature

“…DCs and ECs, according to the literature data, constitute 0.04-0.7% and 0.1-1% of all primary intracranial tumors, respectively [10,11]. DCs are thought to be more common in the females and ECs -in the males.…”

“…Depending on location and organs involved, they pose a challenge for neurosurgeons, dermatologists and cosmetologists, general surgeons, gynecologists, pediatricians, ophthalmologists, ENT specialists and, ultimately, pathologists, if only due to ambiguous diagnostic criteria and inconsistent nomenclature. DTs of virtually any location have been described, including orbit [1], intracranial [2], intralingual [3], parotid [4,5], floor of the mouth [6], testes [7], ovaries [8], omentum [9] and nose [10] to name just a few.…”

Midline Approach to Pediatric Nasofrontal Dermoid Cysts

“…Furthermore, recurrence has been estimated at 50% to 100% if resection is incomplete. 5 Historically, the vertical midline approach has been widely supported in the literature and was the most commonly used approach, yielding satisfactory results with minimal recurrence.…”

Closed rhinoplasty approach for excision of nasal dermoids

“…This must not be compromised by aesthetic considerations. Recurrence rates of 50–100 per cent have been reported in cases in which dermal components were incompletely removed 10 , 24 . Recurrence may result in infection, further surgery and a far worse cosmetic outcome, or, worse still, may potentially lead to ocular or intracranial complications.…”