Congenital multiple clustered dermatofibroma

Abstract

Multiple clustered dermatofibroma (MCD) is a rare tumour which usually appears during the first and second decades of life. We report a man in whom the MCD was congenital, although during the first few years of his second decade it extended to involve a broad zone on the left hip, gluteal region and upper thigh.

Multiple, Clustered Dermatofibroma: A Rare Clinical Variant of Dermatofibroma

“…MCDF generally has an onset in the first or second decade of life, with one report of congenital onset. 19 New lesions develop over months to years. This evolutionary behavior may manifest as expansion of the DF plaque 15 or, as in our case and others, 16,18 in the appearance of satellite lesions.…”

“…Six cases of histologically confirmed DF fitting this morphology have been reported, including the current case. [15][16][17][18][19] When considered in aggregate, these cases exhibit substantial similarity in clinical features and behavior, which may warrant recognition of multiple, clustered DF (MCDF) as a distinct clinical variant of DF. MCDF occurs in both sexes, and it appears to have a predilection for the lower extremity, as all reported cases of MCDF developed in the hip/thigh region.…”

A Case of Idiopathic Dermatofibromatosis

“…[22][23][24][25][26][27][28] Tablo 1'de literatürde 18 yaş ve altında bildirilen multipl dermatofibrom olguları görül-mektedir. 4,6,[29][30][31] Literatür taranarak elde edilen 18 yaş altı MED tanılı olgular incelendiğinde cinsiyet açısın-dan fark saptanmamış olup, olguların hiçbirinde eşlik eden hastalık veya sistemik tedavi kullanımı bildirilmemiştir. Lokalizasyonun ağırlıklı olarak gövde ve ekstremite dağılımlı olduğu gözlen-miştir.…”

Multiple Clustered Dermatofibromas on a Superficial Venous Thrombosis in a Kidney-Transplanted Patient

“…Triggering factors as insect bites, jelly fish bites and surgery have been incriminated in some cases. However, trauma as a triggering event in the appearance of MCD remains controverted [2].…”