A case of parachute deformity of the mitral valve, a rare congenital form of mitral stenosis characterized by insertion of the chordae tendineae into a single posterior papillary muscle, is described in an 11-year-old girl. The eleven other cases in the English literature are reviewed.Shone, Sellers, Anderson, Adams, Lillehei, and Edwards (1963) descri;bed a developmental deformity of the mitral valve characterized by insertion of the chordae tendineae into a single papillary muscle, producing a funnel-shaped valve which is to some degree stenotic. They employed the term 'parachute' first used by Edwards (1961), and noted an association with other leftsided cardiac deformities. We have discovered only 11 such cases published in English. We record the finding of such a parachute mitral valve in association with a bicuspid stenotic aortic valve.To avoid possible confusion the term 'parachute mitral valve' is used throughout this paper in the way originally used by Edwards, and not to describe a ballooned mitral valve cusp (Hudson, 1965).
CASE REPORTOur patient was a white girl, who was first found to have a heart murmur during a routine school medical examination at the age of 5 years. She was slightly more short of breath on exertion than her fellows, and when aged 6 was first admitted to the Cardiac Unit, Papworth Hospital, for assessment. She was normally developed for her age. Her right brachial blood pressure was 90/60 mm. Hg, and her pulse was soft and regular. Her apex beat was described as forceful but not displaced. An ejection click preceded a loud systolic murmur and thrill of maximal intensity in the second left intercostal space adjacent to the sternum. Only one element of the second sound was heard. No murmurs indicative of mitral valve disease were heard at this time or subsequently.The electrocardiogram showed sinus rhythm and was within normal limits. The chest radiograph was suggestive of left ventricular enlargement. No enlargement of the left atrium was apparent.Later that year she developed measles, and thereafter suffered from recurrent respiratory infections. At the age of 7 the diagnosis of aortic stenosis was confirmed by direct left ventricular puncture. The peak systolic gradient was 40 mm. Hg.At the age of 11 she was admitted to Huntingdon Hospital with a three-day history of fever, dyspnoea, and cough productive of purulent, blood-stained sputum. She was extremely ill, with a rapid, feeble pulse and the signs of right basal consolidation. The electrocardiogram showed first degree heart block (P-R interval 0-24 sec.) and T-wave inversion in the left ventricular precordial leads. She was treated for pneumonia and heart failure without response, and on the eleventh hospital day was transferred to the Cardiac Unit, Papworth Hospital. By this time she was dyspnoeic and pallid, with cold cyanosed extremities. The apex beat was felt in the anterior axillarv line, and a soft systolic murmur and gallop rhythm were audible. Signs of consolidation were evident at bo,th lung bases and the liver ed...