Congenital midline palatomandibular bony fusion with a mandibular cleft and a bifid tongue

Rao, Seema; Oak, Sanjay; Wagh, Milind S.; Kulkarni, Bharati

doi:10.1016/s0007-1226(97)91328-x

Cited by 34 publications

(13 citation statements)

References 15 publications

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“…It is difficult to standardize the treatment because the disease is rare, and it is often part of a malformation syndrome [6]- [8]. In all cases, early treatment is essential.…”

Section: Discussionmentioning

confidence: 99%

Complete Fusion of the Maxillamandibular: Report of a Rare Case and Review of the Literature

Chabbak¹,

Rafik²,

Chlihi³

2015

IJOHNS

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The maxillomandibular fusion is a very rare condition, with no more than forty cases described in the literature. Adhesions of bone and/or soft tissue between the mandible and maxilla manifest themselves in the inability to open the mouth added to impacts on mandibular growth, nutrition and speech. This condition can be isolated or, when congenital, associated with other anomalies such as cleft lip and palate, aglossia, or Van der Woude syndrome. In the present paper, we report a case of maxillomandibular fusion treated in our department at University Hospital, between February 2011 and June 2014. The case is a congenital maxillomandibular fusion in a two-year-old infant, associated with a syndrome of Van der Woude. We discuss the diagnostic and treatment difficulties on the anaesthetic and surgical levels and the action to be taken to avoid recurrence. To date, some classifications have been suggested in the literature, but there is no standard treatment protocol. Early treatment is necessary to allow freedom of the upper airway, and ensure proper nutrition and good growth of facial bones. The success of surgery is conditioned by an adequate physiotherapy follow-up likely to guarantee the non-recurrence of the lesion.

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“…It is difficult to standardize the treatment because the disease is rare, and it is often part of a malformation syndrome [6]- [8]. In all cases, early treatment is essential.…”

Section: Discussionmentioning

confidence: 99%

Complete Fusion of the Maxillamandibular: Report of a Rare Case and Review of the Literature

Chabbak¹,

Rafik²,

Chlihi³

2015

IJOHNS

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“…[15] Associations have also been postulated with cleft palate, mandibular cleft, midline palatomandibular bony fusion and cervical vertebrae. [16]…”

Section: Discussionmentioning

confidence: 99%

Isolated congenital bifid tongue

Surej

Kurien

Sivan

2010

Natl J Maxillofac Surg

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Human growth and development is a meticulously planned and precisely executed process. Even a mild disturbance can have clinically significant manifestations later on. Even today, ancient beliefs and practices override/delay patient's aspiration for seeking treatment as seen in the case report presented here. Congenital bifid tongue in association with various other orofacial abnormalities has been reported, many of which have been linked to various syndromes. But congenital bifid tongue occurring in the absence of other orofacial abnormalities is very rare. Here, we discuss a case of bifid tongue involving the anterior one-third of tongue, reported in a 45-year-old male patient unusually with no other intraoral abnormalities.

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“…They considered persistence of the buccopharyngeal membrane or aminotic constriction bands in the region of the developing branchial arches. Credence was also given by Rao et al (1997) to environmental insults like meclozine and large doses of vitamin A as the possible cause of this condition. Dawson et al (1997) reviewed five cases which had no evidence to support familial influence, environmental insult like drugs or consanguinity.…”

Section: Discussionmentioning

confidence: 99%