Congenital Malformations of the Ear Analysis of 94 Operations

Jahrsdoerfer, Robert A.

doi:10.1177/000348948008900410

Cited by 82 publications

(60 citation statements)

References 1 publication

Supporting

Mentioning

Contrasting

Unclassified

Order By: Relevance

“…The degree of microtia is parallel to the anomalous route of the facial nerve [13]. In our study, we observed that 28.1% of patients had facial canal dehiscence, while 2.9% of patients had temporary facial paralysis.…”

Section: Problems Concerning the Facial Nervesupporting

confidence: 47%

Outcomes, Complications and Management of the Congenital Aural Atresia Surgery

Kuşçu¹,

Tahir²,

Günaydın³

et al. 2014

IJOHNS

View full text Add to dashboard Cite

Congenital aural atresia is characterized by aplasia of the external auditory canal (EAC), often associated with abnormalities of the auricula (microtia), the middle ear, and, occasionally, the inner ear structures. The aim of this study is to evaluate the surgical challenges, complications and long term results of congenital aural atresia (CAA) surgery. Records of 103 patients who underwent surgery because of congenital aural atresia were reviewed between 1992 and 2012 in a tertiary referral center. Audiological and surgical events were observed. Surgical technique, incision type, graft material and long term results were noted. Postoperative visit records and audiograms were investigated. Many types of ossicular chain abnormalities such as absence of an ossicle, deformity of an ossicle or ossicular block were observed. Facial canal dehiscence or abnormal location of the facial nerve was seen in 33.9% of patients. Closure of the air-bone gap (ABG) to 30 dB or less at short-term follow-up occurred in 63.1% of patients. Major complications were as follows: restenosis of the external ear canal, hearing loss, facial paralysis, iatrogenic cholesteatoma and perforation of the graft. The air-bone gap cannot be totally closed in all aural atresias, and there is also the chance of sensorineural type hearing loss. Success of the surgery depends on accompanying abnormalities like unexpected route or dehiscence of facial nerve, status of the ossicular chain and middle ear cleft and surgical techniques. Long term results of congenital aural atresia surgery are encouraging and promising.

show abstract

Section: Problems Concerning the Facial Nervesupporting

confidence: 47%

Outcomes, Complications and Management of the Congenital Aural Atresia Surgery

Kuşçu¹,

Tahir²,

Günaydın³

et al. 2014

IJOHNS

View full text Add to dashboard Cite

show abstract

“…Although congenital anomalies of the ossicles without malformations of the external ear are not common, high resolution CT scanning of the (2) 5b0Anterior and posterior crura fusion without oval window (1) 5c0No stapes and no oval window (2) 5d0No stapes and no oval window without incus long process (1) 5e0No stapes and no oval window with incus long process fused to promontrium (1) temporal bone and exploratory tympanotomy have increased their identification. Many prior studies [4,6Á12] have reported on congenital anomalies of the ossicles without deformities of the external ear in relation to their etiology and surgical results.…”

Section: Discussionmentioning

confidence: 99%

“…Minor congenital anomalies are restricted to the middle ear, while major congenital anomalies can involve the middle ear, external meatus, and the auricle [1,2]. Ossicular anomalies may occur with a normal tympanic membrane and external auditory canal.…”

Section: Introductionmentioning

confidence: 99%

Isolated congenital ossicular anomalies

Park

Choung

2009

Acta Oto-Laryngologica

View full text Add to dashboard Cite

Conclusions. Isolated congenital ossicular anomalies are diverse. Our proposed modified Teunissen and Cremers classification will be helpful for the evaluation of congenital ossicular anomalies as well as the prediction of surgical outcome. Objectives. The aim of this study was to describe isolated congenital ossicular anomalies encountered in patients who have normal eardrums and to evaluate their surgical outcome based on their classification. Patients and methods. A total of 78 patients (94 ears) with congenital ossicular anomalies were reviewed. The preoperative and postoperative audiological findings, surgical findings, and temporal bone CT results were analyzed. Results. Twenty-one types of ossicular anomalies were identified in this study. A stapes footplate fixation was the most common anomaly and this was usually bilateral. However, the anomalies that were associated with the incus and malleus were usually unilateral. The congenital ossicular anomalies were classified into five types according to the status of the stapes footplate. Using this modification of a prior classification system, the more severe anomalies of the stapes footplate could be identified, and the worst postoperative hearing result could be predicted.

show abstract

“…The Jahrsdoerfer radiological scoring system, based on the findings of HRCT of the temporal bone and the appearance of the external ear, provides a very important preoperative guideline for selecting patients for canaloplasty and tympanoplasty [4][5][6][7] . However, the auditory ossicle and the canal for facial nerve are such fine structures that HRCT provides limited investigation of spatial relationships between the most important structures.…”

Section: Discussionmentioning

confidence: 99%

“…However, accessing the ossicles during the operation is challenging, due to unpredictable anatomy and lack of valid intra-operative guidance. Although preoperative high-resolution computed tomography (HRCT) is routinely adopted to evaluate the malformation and make surgery plans, an unsatisfactory achievement ratio has been obtained [4][5][6][7] . This study is to radiologically investigate the spatial relationship between the TBR/CA and the ossicles, using the multi-planar reconstruction (MPR) technique, which allows reconstruction of HRCT views from any aspect, thus providing guidance for canaloplasty of the external auditory meatus and tympanoplasty operation.…”

Section: Introductionmentioning

confidence: 99%

Radiological Investigation of the Variance of Ossicular Position in Microtic Ears

Zhou¹,

Wang²,

Han³

et al. 2014

Int Adv Otol

View full text Add to dashboard Cite

OBJECTIVE:To radiologically investigate the malformations in microtic ears so as to provide assistance for canaloplasty of the external auditory meatus and tympanoplasty operation. MATERIALS and METHODS:High-resolution computed tomography (HRCT) data of 48 patients with unilateral congenital microtia and aural atresia were studied. Multi-planar reconstruction (MPR) was performed to investigate the anatomic anomaly. The oblique axial and coronal planes were evaluated, on which the tympanic bone remnant was shown and the ossicular mass appeared with the largest size. The angles between the oblique axial/coronal planes and standard axial/coronal planes were measured and named α and β. The thickness of the atresia plate was measured on the oblique planes. The measurements in the microtic ears were compared with data from the normal side and 40 ears in 20 control individuals without ear malformations as well. RESULTS:In most of the microtia patients, the α angle in the affected side (19.78°±7.42°) was larger than the α angle in the normal side (15.30°±4.60°), while the β angle in the affected side (16.77°±13.43°) was smaller than the β angle in the normal side (27.46°±6.87°). The thickness of the atresia plate was less than the thickness of the cribriform area in the normal side. A significant correlation was found between the Marx classification and the thickness of the atresia plate. CONLUSION:HRCT evaluation using MPR is an important complement for the Jahrsdoerfer scoring system. The investigation is of great realistic significance. Preoperative measures for individual patients can provide guidance for canaloplasty and tympanoplasty operation.

show abstract

Congenital Malformations of the Ear Analysis of 94 Operations

Cited by 82 publications

References 1 publication

Outcomes, Complications and Management of the Congenital Aural Atresia Surgery

Outcomes, Complications and Management of the Congenital Aural Atresia Surgery

Isolated congenital ossicular anomalies

Radiological Investigation of the Variance of Ossicular Position in Microtic Ears

Contact Info

Product

Resources

About