Congenital lobar emphysema and sequestration—treatment by embolization

Nayar, P. M.; Thakral, C. L.; Sajwani, Mohammed Jaffer

doi:10.1007/s00383-005-1462-1

Cited by 8 publications

(3 citation statements)

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“…(46)(47)(48) The principal cause of congenital lobar emphysema is developmental deficiency of bronchial cartilage, (5,46,49) which occurs in approximately 25% of cases. Obstruction of a lobar bronchus occurs in another 25% of cases and is generally caused by idiopathic bronchial stenosis that leads to a check-valve mechanism, which can also be triggered by mucus plugging or vascular changes.…”

Section: Congenital Lobar Emphysemamentioning

confidence: 99%

“…(4,46) Congenital lobar emphysema is characterized by hyperinflation of a lung lobe caused by air trapping, resulting in distension of the lobe and causing a mass effect that compresses the remaining lobes and causes mediastinal shift (Figure 4), leading to hemodynamic changes. (47,48,50) Congenital lung malformations J Bras Pneumol. 2011;37(2):259-271…”

Section: Congenital Lobar Emphysemamentioning

confidence: 99%

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Malformações pulmonares congênitas

2011

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Congenital lung malformations are rare and vary widely in their clinical presentation and severity, depending mostly on the degree of lung involvement and their location in the thoracic cavity. They can manifest at any age and can be the source of significant morbidity and mortality in infants and children. Individuals with congenital lung malformations can present with respiratory symptoms at birth or can remain asymptomatic for long periods. Recently, there has been an increase in the early diagnosis of these malformations, a change that is attributable to the routine use of prenatal ultrasound. The clinical manifestation of these malformations varies from respiratory distress in the immediate postnatal period to an incidental finding on chest X-rays. Early diagnosis and prompt treatment offer the possibility of absolutely normal lung development. The treatment of asymptomatic patients with lung malformations is controversial, because the prognosis of these diseases is unpredictable. The management of these lesions depends on the type of malformation and symptoms. Because of the risk of complications, most authors recommend resection of the lesion at the time of diagnosis. Lobectomy is the procedure of choice and yields excellent long-term results. This article describes the principal congenital lung malformations, their diagnosis, and the controversies regarding treatment.Keywords: Cystic adenomatoid malformation of lung, congenital; Bronchopulmonary sequestration; Pulmonary surgical procedures; Diagnosis. ResumoAs malformações congênitas do pulmão são raras e variam muito na sua forma de apresentação clínica e gravidade, dependendo principalmente do grau de envolvimento pulmonar e de sua localização na cavidade torácica. Elas podem se manifestar em qualquer idade e podem ser fonte de importante morbidade e mortalidade em lactentes e crianças. Os indivíduos com malformações congênitas do pulmão podem apresentar sintomas respiratórios ao nascimento, enquanto outros podem permanecer assintomáticos por longos períodos. Atualmente, com o uso rotineiro da ultrassonografia pré-natal, vem ocorrendo um aumento no diagnóstico mais precoce dessas malformações. A manifestação clínica dessas malformações varia desde uma disfunção respiratória pós-natal imediata a um achado acidental na radiografia de tórax. O diagnóstico precoce e o tratamento imediato oferecem a possibilidade de um desenvolvimento pulmonar absolutamente normal. Quando assintomáticos, a conduta para o tratamento dos pacientes com malformações pulmonares ainda é controversa, uma vez que o prognóstico dessas afecções é imprevisível. O manejo dessas lesões depende do tipo de malformação e de sintomas. Devido ao risco de complicação, a maioria dos autores sugere a ressecção da lesão no momento em que essa é identificada. A lobectomia é o procedimento de escolha, fornecendo excelentes resultados a longo prazo. Este artigo descreve as principais malformações pulmonares congênitas, seu diagnóstico e controvérsias quanto o tratamento. (5) is covered by ...

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Section: Congenital Lobar Emphysemamentioning

confidence: 99%

Section: Congenital Lobar Emphysemamentioning

confidence: 99%

Malformações pulmonares congênitas

2011

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“…CLE is characterized by progressive lobar hyperinflation, caused by air trapping in a collapsed airway, resulting in distension of the lobe and a mass effect that compresses the other lobes and shifts the mediastinum ( 6 , 7 ) . There is no alveolar destruction ( 11 ) .…”

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confidence: 99%