Congenital isolated tricuspid regurgitation in an adult

Sakai, Kichiro; Inoue, Yasuo; Osawa, Mikio

doi:10.1016/0002-8703(85)90099-7

Cited by 9 publications

(6 citation statements)

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“…11 One group of patients manifest severe, and sometimes fatal, disease in the fetal 16 or neonatal 8 " 11 periods, while another group presents later in childhood or in adulthood with a less fulminant symptomatology. 17 Occasionally, the severe symptoms of tricuspid regurgitation in young patients may resolve spontaneously or with medical treatment, 18 which suggests that the gravity of tricuspid dysplasia in neonates and fetuses may be in part a function of the unique physiologic conditions of these age periods. In the fetus, the right heart is dominant and functions at systemic pressures.…”

Section: Discussionmentioning

confidence: 99%

Asymmetrically short tendinous cords causing congenital tricuspid regurgitation: improved understanding of tricuspid valvar dysplasia in the era of color flow echocardiography

et al. 1999

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Section: Discussionmentioning

confidence: 99%

Asymmetrically short tendinous cords causing congenital tricuspid regurgitation: improved understanding of tricuspid valvar dysplasia in the era of color flow echocardiography

et al. 1999

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“…Another possible diagnosis, Ebstein's anomaly, is a congenital cardiac anomaly causing tricuspid valve regurgitation with displacement of posterior and anterior tricuspid leaflet insertion into the right ventricle, with evidence of atrialization of the right ventricle, which is a diagnostic feature for this anomaly and readily seen by twodimensional echocardiography. 7 Isolated congenital tricuspid insufficiency is another rare possible diagnosis, with some valvular deformity and is usually included with Ebstein's anomaly. 8 It was unlikely in our patient because his valve was of normal morphology.…”

Section: Discussionmentioning

confidence: 99%

Arrhythmogenic Right Ventricular Dysplasia (ARVD) in Childhood: Case Report with a Review of the Literature

Jarallah

1997

Ann Saudi Med

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AS Al Jarallah, Arrhythmogenic Right Ventricular Dysplasia (Arvd) in Childhood: Case Report with a Review of the Literature. 1997; 17(3): 350-353 Over the last few decades of advances in the field of cardiology, many newly identified diseases have been described. One of these newly recognized conditions was arrhythmogenic right ventricular dysplasia (ARVD), which was first described in 1978 by Frank et al. 1 The clinical spectrum of this condition was described by Marcus et al. in 1982. 2 Estimates of the prevalence of ARVD vary sharply in the literature. Thiene et al. found a startling 20% incidence of ARVD in a study of sudden deaths in young adults originating from northeast Italy. 3 In contrast, in two retrospective studies of sudden deaths in young American adults, the incidence of ARVD was found to be 0.5%-3.0%. 4 In this condition, areas of fatty and fibrous tissues replace the normal myocardium of the right ventricle. The involved myocardium evokes ventricular arrhythmias of right ventricular origin. The diagnosis of ARVD in the past was based on the presence of ventricular arrhythmia with left bundle branch block configuration and morphologic changes or motion abnormalities in the free wall of the right ventricle. 2 Recently, standardized diagnostic criteria have been proposed, based on the presence of major and minor criteria encompassing structural, histological, electrocardiographic, arrhythmia, and genetic factors. 5 Although the long-term prognosis of ARVD is generally good, the prevalence is unknown because of its rarity, especially in the pediatric age group. A male child with ARVD is reported here, with a review of the literature. Case ReportA 12-year-old boy presented with an 18-month history of progressive shortness of breath and recurrent vomiting. Nine months prior to admission, he was seen in a private clinic with severe dyspnea and tachycardia (heart rate of 216 beats/min), where he was diagnosed with heart failure and treated with digoxin, furosemide and spironolactone. There was no history of rheumatic fever or endocarditis and no family history of heart disease.General examination revealed a puffy child, mildly dyspneic, and pink in color. Weight was in the 50th percentile, height in the 10th percentile, temperature was normal, respiratory rate was 22 per minute. Pulse was 110 per minute, regular, good volume, with no radio-femoral delay. Blood pressure was 110/75 mmHg in the right upper arm. Precordial examination revealed no chest deformity, with quiet precordium, no thrill. First and second heart sounds were muffled, third heart sound was audible (gallop rhythm) with a grade 3/6 pansystolic murmur at the left lower sternal border and the lung fields were clear with equal air entry. Abdomen was slightly distended with mild ascites and tender hepatomegaly (6 cm below the right costal margin). There was pitting edema involving both lower limbs.Chest x-ray showed globular enlargement of the heart (cardiothoracic ratio 70%) (Figure 1). The 12-leads electrocardiography showed sinus rh...

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“…The chest radiograph shows right atrial and right ventricular enlargement and normal pulmonary vascularity. 1,11,17,[29][30][31][32][33][34][35][36][37][38][39][40] An electrocardiograph usually shows right axis deviation, right atrial enlargement, right bundle branch block, and first degree atrioventricular block, 1,27,29 and sometimes prolonged corrected QT interval. 29 There may be sinus tachycardia, supraventricular extrasystoles, and atrial fibrillation.…”

Section: Investigationsmentioning

confidence: 99%

“…29 There may be sinus tachycardia, supraventricular extrasystoles, and atrial fibrillation. 11,17,[29][30][31][32][33][34][35][36][37][38][39][40] Cardiac catheterisation reveals elevated right atrial pressure, a pronounced ''V'' wave of tricuspid regurgitation, normal right ventricular pressure, and sometimes a right-to-left shunt at the atrial level. 1,[10][11][12][13][14][15][33][34][35][36][37][38] However, cardiac catheterisation is not required to make a diagnosis in the present day.…”

Section: Investigationsmentioning

confidence: 99%

“…Hypoplastic anterior tricuspid leaflet Shibata et al, 25 Abrams et al, 27 Mantovani et al 30 3 Absent anterior tricuspid leaflet Sakai et al, 35 Pernot et al 37 4 Fenestration in posterior tricuspid leaflet Hung et al 36 5 Aberrant chordae Aaron et al, 1 Boon et al, 21 Eichhorn et al, 29 Kobza et al 32 6 Non-aberrant short chordate Honjo et al, 24 Abrams et al, 27 McElhinney et al, 31 Reddy et al 39 7 Absent chordae Anita and Osunkoya, 16 Honjo et al, 24 Abrams et al, 27 Katogi et al, 28 Yang et al, 38 Reddy et al 39 8 Elongated chordate Ootaki et al 22 9 Absent anterior papillary muscle Anita and Osunkoya, 16 Barr et al, 17 Katogi et al, 28 Yang et al 38 10 Absent commissure Katogi et al, 28 Mantovani et al 30 11 Annular dilatation Anita and Osunkoya, 16 Barr et al, 17 Motoyoshi et al, 23 Shibata et al, 25 Abrams et al, 27 Aoyogi et al, 34 Reddy et al, 39 Girad et al 40 12 Unguarded tricuspid valve Kanjuh et al, 18 Green et al, 19 Kilic et al, 43 Ozkutlu et al, 44 Klein, 52 Anderson et al 53 13 Double or...…”

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confidence: 99%

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Congenital tricuspid regurgitation: review and a proposed new classification

2010

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Congenital tricuspid regurgitation is an uncommon clinical entity with wide anatomical variations. The severity of disease dictates the presentation in infancy, childhood, or adulthood. Tricuspid valve repair is the ideal treatment whenever feasible, especially in children. We propose a new classification for congenital tricuspid regurgitation, which not only includes the anatomical variations, but can also help the surgeon in deciding on the best strategy for management.

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Congenital isolated tricuspid regurgitation in an adult

Cited by 9 publications

References 1 publication

Asymmetrically short tendinous cords causing congenital tricuspid regurgitation: improved understanding of tricuspid valvar dysplasia in the era of color flow echocardiography

Asymmetrically short tendinous cords causing congenital tricuspid regurgitation: improved understanding of tricuspid valvar dysplasia in the era of color flow echocardiography

Arrhythmogenic Right Ventricular Dysplasia (ARVD) in Childhood: Case Report with a Review of the Literature

Congenital tricuspid regurgitation: review and a proposed new classification

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