“…About 50 per cent of the affected children die of cardiac or respiratory problems (Bui et al, 1984). The signs of the associated ectodermal dysplasia are constant features of EVC: sparse hair, underdeveloped and dysplastic nails (Lynch et al, 1968), and abnormal, missing, or even natal teeth. Fusion of the gums of the maxilla and the upper lips and obliteration of the sulcus gingivolabialis are also frequently seen (Ellis and Andrew, 1962).…”