Congenital Genitourinary Hemangiomas in a Patient with the Klippel-Trenaunay Syndrome: Management with the Neodymium:Yag Laser

Hockley, Nancy M.; Bihrle, Richard; Bennett, Richard; Curry, Jon

doi:10.1016/s0022-5347(17)41061-5

Cited by 23 publications

(20 citation statements)

References 18 publications

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“…Vesical hemangiomas have an incidence of less than 1% of the organ's primary tumors, being, however, the most common connective tissue benign tumor in bladder (3). Painless gross hematuria is a characteristic of this type of tumor, as it was observed in the present case (2).…”

Section: Discussionsupporting

confidence: 69%

Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome

Favorito¹

2003

Int. braz j urol.

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Klippel-Trenaunay-Weber syndrome is characterized by cutaneous hemangiomas, varicosity and bony hypertrophy of extremities. Urinary tract hemangiomas may occur in 3 to 6% of these patients. This work intends to report a case of a patient with a huge vesical hemangioma, who presented this syndrome.A 5 year-old boy with Klippel syndrome sought our services due to 3 episodes of gross hematuria in the past 30 days. Excretory urography and computerized tomography were performed, indicating the presence of a swelling in vesical dome. An exploratory cystotomy was conducted and the dark colored mass in vesical dome was excised by partial cystectomy. The histopathologic finding confirmed that it was a vesical hemangioma. Though rare, urinary tract hemangiomas must always be considered in patients with Klippel-Trenaunay syndrome.

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Section: Discussionsupporting

confidence: 69%

Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome

Favorito¹

2003

Int. braz j urol.

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“…Hematuria is a common symptom in patients with genitourinary and pelvic vascular malformation necessitating therapeutic intervention. Hematuria as a presenting symptom has been reported in children [1][2][3], but massive hematuria in adults associated with KTS is rare [7][8][9]. We report 2 cases of hematuria in adults with KTS.…”

Section: Introductionmentioning

confidence: 84%

“…There have been 3 case reports of significant hematuria in adult patients with KTS [7][8][9]. In 2 patients, the upper tract was the source of bleeding.…”

Section: Discussionmentioning

confidence: 99%

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Massive Hematuria in Adults with Klippel-Trenaunay Syndrome Associated with Vascular Malformation of the Bladder

Shekarriz¹,

Upadhyay²,

Smith³

et al. 2000

Urol Int

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Although hematuria has been reported in children with Klippel-Trenaunay syndrome, it is a rare presentation in the adult population. Two cases of massive hematuria in adults with Klippel-Trenaunay syndrome are reported here. A unique feature was venous malformations of the bladder which were responsible for massive recurrent bleeding in 1 patient. The clinical presentation and management are discussed. Conservative endoscopic and arteriographic control seems to be appropriate as initial management in these patients.

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“…Most angiomatous tumors have been located at the glans penis: only 4 out of 19 involved the penile shaft. Penile hemangiomas may occur as iso lated lesions or in association with cutaneous and visceral vascular malformations as in the Klippel-Trenaunay-Weber syndrome [17]. This syndrome is characterized by hemangiomatous involvement pri marily of the lower extremities with varicose veins, soft tissue hyper trophy of the involved extremity sometimes requiring amputation.…”

Section: Biopty Gun For Corpus Cavemosum Biopsymentioning

confidence: 99%