Congenital Developmental Arrest of the Lung

Borja, Alonzo R.; Ransdell, Herbert T.; Villa, Sergio

doi:10.1016/s0003-4975(10)65608-1

Cited by 25 publications

(13 citation statements)

References 15 publications

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“…Diagnosis may be established with help of chest x-ray, CT thorax, fiber optic bronchoscopy and if possible pulmonary angiography and bronchography. 4,5 Thomas et al suggested that CT is more useful than bronchography in assessing the hypoplastic lung, especially for the purposes of its surgical removal. 6 Radiographic findings in cases of hypoplasia are similar and characterized principally by almost total absence of aerated lung in one hemi thorax.…”

Section: Discussionmentioning

confidence: 99%

Unilateral Lung Hypoplasia Presenting in Adolescence: A Case Report

Paul¹,

Bharti²,

Kazal³

2015

jemds

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Pulmonary hypoplasia is a rare congenital anomaly, which is frequently associated with other congenital anomalies. Most patients have recurrent episodes of wheezing or pneumonia and severe respiratory distress leading to chronic respiratory failure whereas some may be asymptomatic. Although it is usually diagnosed in infancy and childhood, some cases do not show any symptoms until the adolescent ages. In adolescents and adults with unilateral hypolucent lung, pulmonary hypoplasia should always be kept in mind.

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Section: Discussionmentioning

confidence: 99%

Unilateral Lung Hypoplasia Presenting in Adolescence: A Case Report

Paul¹,

Bharti²,

Kazal³

2015

jemds

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“…The incidence of agenesis has been estimated to be 1 in 10,000-15,000 autopsies (Ellis 1917;Olcott and Dooley 1943;Krivchenya et al 2007). Borja et al (1970) reported four cases among 114,569 admissions (1in 28,642) in a hospital over 19 years. The difference between genders was 3:2 (males to females) (Marioni 1962), and the right to left ratio was 1:3 (Ingram et al 1950).…”

Section: Agenesis Aplasia and Hypoplasia Of The Lungmentioning

confidence: 99%

Lungs

Watanabe¹

2016

Bergman's Comprehensive Encyclopedia of Human Anatomic Variation

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“…2,7,8 In patients with pulmonary aplasia, the poor mucociliary clearance of the rudimentary bronchial bud may provide a reservoir for repeated infection of the contralateral lung. 9 Survival of patients with pulmonary agenesis or aplasia into adulthood is possible. 2,3 Such patients may have relatively little functional impairment and may be asymptomatic.…”

Section: Clinical Manifestationsmentioning

confidence: 99%

Unilateral Thoracic Opacification With Volume Loss

Elicker

Leung

Reddy

et al. 2006

Clinical Pulmonary Medicine

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Pulmonary agenesis is a rare congenital thoracic disorder that affects approximately one in 10,000 individuals and shows no gender preference. This disorder is characterized by complete absence of the bronchi and vessels, and pulmonary parenchyma; pulmonary aplasia may show a small rudimentary bronchus unaccompanied by vessels or alveoli. Many patients with pulmonary agenesis or aplasia die in infancy of respiratory infections, respiratory insufficiency, or associated congenital disorders. The thoracic imaging appearance of pulmonary agenesis or aplasia consists of complete opacification of one hemithorax with severe volume loss evidenced by extensive shift of the cardiomediastinal structures toward the affected side. The imaging appearance of pulmonary agenesis or aplasia must be distinguished from a number of other conditions characterized by extensive pulmonary parenchymal volume loss such as pulmonary hypoplasia, mainstem bronchial obstruction with complete collapse of one lung, extensive fibrothorax, and pneumonectomy. The complete absence of lung tissue and a pulmonary artery on the affected side confirms the diagnosis and may be best appreciated on thoracic computed tomography.

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Congenital Developmental Arrest of the Lung

Cited by 25 publications

References 15 publications

Unilateral Lung Hypoplasia Presenting in Adolescence: A Case Report

Unilateral Lung Hypoplasia Presenting in Adolescence: A Case Report

Lungs

Unilateral Thoracic Opacification With Volume Loss

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