Congenital Cystic Lung Disease: Diagnostic and Therapeutic Considerations

Abstract

Congenital lung cysts such as congenital cystic adenomatoid malformation, pulmonary sequestration, congenital lobar emphysema, and bronchogenic cysts are rare but fascinating anomalies of lung development. While there are many similarities in terms of their presenting features, there are particular differences between the diagnostic groups that are important to highlight, especially in relationship to approaches to imaging and long-term outcome. A case of each entity is presented with an emphasis on the contemporary approach to diagnostic investigations and therapeutic options.

Congenital bronchial atresia in infants and children

“…Interestingly, there is little in the literature suggesting that CBA accounts for CCLD [11][12][13][14]. We believe the discrepancy between the previous reports and this series attribute to difficulties in pathological diagnosis of CBA.…”

“…It has been reported that CBA frequently affects the left upper lobe and is incidentally diagnosed in asymptomatic young adults [1,4,5]. However, there are only a few case reports of CBA diagnosed in childhood [6][7][8][9][10], and there is little in the literature suggesting that CBA accounts for congenital cystic lung disease (CCLD) [11][12][13][14]. Here, we describe the clinical and pathological characteristics of CBA in infants and children.…”

Bronchogenic cysts as a cause of infantile stridor: case report and literature review

“…1 Herein, we describe the unusual case of an infant whose airway symptoms were the result of a bronchogenic cyst. 1 Herein, we describe the unusual case of an infant whose airway symptoms were the result of a bronchogenic cyst.…”

Does the use of fentanyl in epidural solutions for postthoracotomy pain management in neonates affect surgical outcome?

“…Conclusion: The addition of fentanyl to epidural infusions of bupivacaine in infants undergoing thoracotomy for resection of CCAM may prolong recovery and increase the incidence of adverse respiratory events without providing a significant analgesic benefit. D 2005 Elsevier Inc. All rights reserved.Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare condition that often requires thoracotomy in infancy for resection of the abnormal lung tissue [1]. The technique of choice at the Children's Hospital of Philadelphia for postoperative pain management in these patients is 0022-3468/$ -see front matter D…”

“…Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare condition that often requires thoracotomy in infancy for resection of the abnormal lung tissue [1]. The technique of choice at the Children's Hospital of Philadelphia for postoperative pain management in these patients is 0022-3468/$ -see front matter D…”