Congenital Cystic Disease of the Lung in Infants and Children (Experience with 57 Cases)

Albassam, A.A.; Al-Rabeeah, Abdullah A.; Alnassar, Sami; Al-Mobaireek, K.; Al-Rawaf, A; Banjer, H.; Al-Mogari, I.

doi:10.1055/s-2008-1072284

Cited by 52 publications

(36 citation statements)

References 17 publications

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“…The prevalence of cystic lesions in the Saudi Arabia study was somewhat comparable to ours regarding the high prevalence of CLE cases (6). Most of our cases with undefined prenatal diagnosis were postnatally diagnosed as CLE (55%).…”

Section: Discussionsupporting

confidence: 59%

“…In our survey, three cases were diagnosed as ELS, two BPS were not defined regarding their subcategory, one case was a hybrid of ELS and CPAM (type 2), and only one case was an ILS. In the study of Langston in Texas, ELSs were almost two times more frequent than ILSs, whereas in the study conducted in Saudi Arabia, such classification was not mentioned (5,6). These lesions equally involved the two hemi-thoraces.…”

Section: Discussionmentioning

confidence: 80%

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An Eleven-Year Review of Congenital Pulmonary Lesions in a Referral Children’s Hospital in Tehran

Shahkar

Sanii

Biglari

et al. 2016

Arch Pediatr Infect Dis

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Background: Congenital pulmonary lesions may be diagnosed through ultrasonographic screenings or be revealed as causes of respiratory distress in the neonatal period and infancy. Less commonly, they are detected as incidental features. Objectives: Our study represents the diversity of congenital pulmonary lesions and their characteristics during an 11-year period in a referral teaching children's hospital in Tehran, the capital city of Iran. Methods: Data from an 11-year period of patients with the final diagnosis of congenital pulmonary lesions in Mofid Children's hospital were reviewed. The data included the prenatal ultrasonographic, postnatal radiographic, and pathologic diagnoses, along with the patient's age, way of presentation, length of hospitalization, and accompanying features and morbidities. Results: Of 37 cases of congenital pulmonary lesions, 28 cases (75%) were boys. Thirty-six cases (97.2%) presented with pure pulmonary signs and symptoms. Of these cases, 16 (43.2%) were neonates, 17 (46%) were infants, and 4 (10.8%) were children. Twentyseven (73%) patients missed the opportunity for early diagnosis. In order of frequency, cases were diagnosed as congenital lobar emphysema (43.5%), congenital cystic adenomatoid malformation (32.5%), pulmonary sequestration (19%), hybrid lesion (2.5%), or bronchogenic cyst (2.5%). Conclusions:In an analysis of retrospective data of 37 congenital pulmonary lesions, male predominance was obvious, as has been found in previous studies.

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Section: Discussionsupporting

confidence: 59%

Section: Discussionmentioning

confidence: 80%

An Eleven-Year Review of Congenital Pulmonary Lesions in a Referral Children’s Hospital in Tehran

Shahkar

Sanii

Biglari

et al. 2016

Arch Pediatr Infect Dis

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“…Surgery is urgent in patients with significant respiratory distress but may be an elective procedure in adults or older children with less symptoms (15,16).…”

Section: Discussionmentioning

confidence: 99%

Intralobar bronchopulmonary sequestration: A case and brief review

Majumdar¹,

Sen²,

Sood³

2018

Southwest J Pulm Crit Care

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Objective: Bronchopulmonary sequestration is a rare congenital abnormality of the lower respiratory tract, seen mostly in children but often in adults. The term implies a mass of lung tissue that has no function and lacks normal communication with the rest of the tracheobronchial tree. Case: A 40-year-old man presented with acute onset of left flank pain for 4 hours. He was born in Yemen and emigrated to the US in 1998; at that time, he had been tested for tuberculosis which was negative. In this admission, he met systemic inflammatory response (SIRS) criteria and had basilar crackles in the left lower lobe of the lung. CT scan revealed a cavitary lesion with air-fluid level in the left lower lobe airspace. There was systemic arterial blood supply to this region arising off the celiac axis. He was diagnosed with an infected intralobar bronchopulmonary sequestration and underwent video-assisted thoracoscopic wedge resection. On follow up 3 months later, he was doing well. Discussion: Pulmonary sequestration is a rare congenital anomaly of a mass of lung tissue, which can have cystic changes and is a very important differential diagnosis of cavities in the lung. Confirmation of diagnosis is by visualization of a systemic vessel supplying sequestrated pulmonary, and this is accomplished by contrast-enhanced CT scan, MRI or invasive angiography. Conclusion:The delay in diagnosis in our patient was due to falling prey to anchoring and availability biases and chasing the diagnosis of tuberculosis in a patient from Yemen with a lower lobe cavitation. Case History of Present Illness:A 40-year-old man with a past medical history of atrial fibrillation presented to the hospital with acute onset of left flank pain for 4 hours, fevers and chills. The pain was sharp and stabbing, pleuritic, non-radiating, and was severe with an intensity of 10/10. He denied extraneous activity or trauma earlier in the day, denied substernal pain, cough, night sweats, weight loss or change in urinary habits. He was born in Yemen and emigrated to the US in 1998; at that time, he was tested for tuberculosis (TB) which was negative. He was known to have a cavitary lesion in left lower lobe since 2005, and had undergone extensive evaluation (imaging, sputum and PPD) which showed no form of tuberculosis. He denied taking prophylactic TB treatment. Annual PPD testing had always been negative.

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“…Standard treatment for acute respiratory distress is surgical resection of the affected lung area [3]. Prognosis and survival with surgery are good [15]. There are many reports of spontaneous regression of pulmonary sequestration and CCAM, similar to these lesions, CLE can decrease in size during pregnancy [5].…”

Section: Discussionmentioning

confidence: 99%

Congenital lobar emphysema with cystic lung abnormality: Antenatal ultrasound appearance

Lee

Jeong

Joo

et al. 2012

Korean J Obstet Gynecol

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A 33-year-old woman at 23 +2 weeks of gestational age was referred for consultation due to the findings of a cyst in the right lung of the fetus. Prenatal ultrasound showed a 3 cm-sized hypoechogenic cyst, suggesting congenital cystic adenomatoid malformation. As the cyst grew and compressed the heart, serial cyst aspirations were performed. The cyst was proved to be congenital lobar emphysema on postnatal histopathologic exam. No other anomaly was found. Only few cases of congenital lobar emphysema (CLE) have been reported up to date and the prenatal diagnosis is extremely rare. Typically, fetal sonographic features of CLE have a bright echogenic lung and, to date, only 3 cases have been reported to have a cystic lesion. We report a case of a fetus with a cystic lung abnormality and postnatally proved congenital lobar emphysema.

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Congenital Cystic Disease of the Lung in Infants and Children (Experience with 57 Cases)

Cited by 52 publications

References 17 publications

An Eleven-Year Review of Congenital Pulmonary Lesions in a Referral Children’s Hospital in Tehran

An Eleven-Year Review of Congenital Pulmonary Lesions in a Referral Children’s Hospital in Tehran

Intralobar bronchopulmonary sequestration: A case and brief review

Congenital lobar emphysema with cystic lung abnormality: Antenatal ultrasound appearance

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