Congenital combined dermal and epidermal melanocytosis: a new entity?

An Unusual Case of Congenital Dermal Melanocytosis

“…In 1999, Grézard et al 4 reported a 45-year-old Caucasian woman with a slowly spreading bilateral congenital pigmentation of the back in a dermatomal distribution from the fourth to the eighth dorsal dermatome that extended laterally to the external part of the breasts. Several authors have also documented cases of isolated small patch forms of congenital dermal melanocytosis [5][6][7] .…”

Case report: Unusual combination of pigmentary lesions

“…Combinations of other pigmentary lesions have also been reported. It includes rare reports of dermal melanocytic lesion superimposed on cafe au lait macules, 9 on blue nevus and on congenital melanocytic nevus 10 . It also includes blue nevus associated with partial unilateral lentiginosis, 11 blue nevus combined with nevus spilus, 12 Spitz nevus with superimposed speckled lentiginous nevus, 13 Giant congenital melanocytic nevus with speckled lentiginous nevus 14 and Cafe au lait spot superimposed on scattered cafe au lait speckles 15 …”

Phacomatosis pigmento-pigmentaria: the state of art

“…Nevus spilus has been reported in association with congenital melanocytic nevus [10], as well as superimposed on or adjacent to other pigmentary disorders [11][12][13][14][15][16][17][18]. Mongolian spot has been described and associated with other pigmentary disorders [19][20][21][22][23][24][25]. Moreover, different associations of nevus anemicus with several pigmental anomalies [7,[26][27][28][29][30][31][32][33][34][35], as well as café au lait macule combined with different disorders of pigmentation [36,37].…”

“…All these previously cited associations have been considered by the authors as occasional associations of two paired nevoid pigmentary disorders and, only in few cases [10][11][12][13][14][15][16][17][18][19][20][21][22][23][24][25][26][27][28][29], explained as examples of twin-spotting phenomenon.…”