Congenital Chylous Ascites: Report of Four Cases and Review of the Literature

Machmouchi, Mahmoud; Amin, A.F.; Lanjaoui, Issam; Jacobs, Arnold; Hatoum, Chimène; Zahrani, Daifullah Al

doi:10.5144/0256-4947.2000.436

Cited by 8 publications

(10 citation statements)

References 24 publications

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“…The most common (45 to 60%) cause is malformation of the lymphatic vessels which can be either atresia or stenosis of the major lacteals. 1,6 Abdominal paracentesis is the most useful diagnostic step 4,5 The findings in our patient were consistent with the diagnosis of chylous ascites. Our patient was diagnosed at the age of three months.…”

Section: Discussionsupporting

confidence: 81%

“…Huang et al diagnosed chylous ascites in a 50-day-old male baby 2 while, Mahmoud et al diagnosed three neonates antenatally at 34, 35 and 37-weeke gestation resp0ectively. 1 The earlier the diagnosis, the better the prognosis. 1 Previous investigators suggested that CCA should be treated conservatively at first.…”

Section: Discussionmentioning

confidence: 99%

“…1 The earlier the diagnosis, the better the prognosis. 1 Previous investigators suggested that CCA should be treated conservatively at first. 7 In a series of 103 Japanese patients 63.5% were cured by conservative treatment.…”

Section: Discussionmentioning

confidence: 99%

“…Congenital chylous ascites (CCA) is defined as the collection of milky fluid rich in triglyceride content inside the peritoneal cavity in children younger than three month of age. 1,2 It can be primary or secondary. 3,4 Primary CCA, is due to mal-development of intraabdominal lymphatic system, while the, secondary is due to neoplastic or inflammatory processes.…”

Section: Introductionmentioning

confidence: 99%

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Congenital chylous as cites in a 3-month-old infant in Zaria: A case report

Abdullahi¹,

Idris²,

Mado³

et al. 2021

Nig. J. Paed.

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Congenital chylous ascites (CCA) is a rare disease that results from the maldevelopment of the intra-abdominal lymphatic system. Due to the rarity of congenital chylous ascites and the lack of standards in diagnosis and therapy, this disease constitutes a medical challenge and individual therapy seems to be extremely important. A 3-month-old girl diagnosed with congenital chylous ascites. She was managed initially with nil per oral, parenteral nutrition, medium chain triglyceride (MCT) containing oil and abdominal paracentesis, followed by octreotide. Medium chain triglyceride formula, the main stay of management was discontinued with gradual reintroduction of breast feeds. This case was selected due to the rarity of CCA and the lack of standards in the diagnosis and therapy.

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Section: Discussionsupporting

confidence: 81%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

See 2 more Smart Citations

Congenital chylous as cites in a 3-month-old infant in Zaria: A case report

Abdullahi¹,

Idris²,

Mado³

et al. 2021

Nig. J. Paed.

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“…In these patients, paracentesis is not only a diagnostic but also a therapeutic tool 3 4. However, this procedure should not be repeated if the baby shows no respiratory distress during conservative treatment, due to the inherent risk of developing hypoproteinemia and accidental perforation of a bowel loop.…”

Section: Discussionmentioning

confidence: 99%

Successful management of congenital chylous ascites with early octreotide and total parenteral nutrition in a newborn

et al. 2012

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Congenital chylous ascites (CCA) is a rare disease that results from maldevelopment of the intra-abdominal lymphatic system. Few cases have been described and no gold standard treatment has been defined so far. Octreotide, a somatostatin analogue, has been used for the treatment of CCA, but always after a failed conservative approach with fasting, total parenteral nutrition (TPN) or medium chain triglyceride (MCT) feeds. We report the case of a newborn with CCA treated by fasting, TPN and octreotide for a period of 15 days until the abdominal distension was successfully reduced at which point treatment was switched to an MCT formula. On day 25 the patient was breastfed and was discharged on day 33. No recurrence of chylous ascites was noted. Our experience highlights the successful treatment with TPN and octreotide as the first step for the conservative approach of CCA in a newborn, reducing the length of treatment and hospitalisation.

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