Congenital bronchobiliary fistula: Management of the involved hepatic segment

Congenital tracheobiliary fistula

“…There are different options to create a connection between the biliary tract and the gastrointestinal system; a Roux-en-Y choledochojejunostomy, a fistula-enteric anastomosis, and in case of an extrahepatobiliary atresia, a portoenterostomy can be performed. Gauderer et al [9] described 3 cases in which the atresia of the common bile duct resulted in an atrophy of the left hepatic lobe. In 2 cases, the involved hepatic segment was managed by resection of the left lobe of the liver.…”

“…Only 25 cases have been reported in the literature [1][2][3][4][5][6][7][8][9]. We present a patient with tracheobiliary fistula and severe respiratory insufficiency needing extracorporal membrane oxygenation (ECMO) to survive.…”

Fístula broncobiliar congénita. Caso clínico

“…No obstante, estos síntomas no son específicos y debe realizarse el diagnóstico diferencial con fístula traqueoesofágica, reflujo gastroesofágico, obstrucción gastrointestinal, fístula gastrointestinal y neumonía aspirativa. [5][6][7] Se han utilizado, para el diagnóstico, la broncoscopía, la broncografía, la colangiografía, la tomografía computada y la resonancia magnética nuclear. Sin embargo, la broncoscopía ha sido la más utilizada (52%) como método diagnóstico, seguido por la colangiografía y la broncografía.…”

Congenital tracheobiliary fistula

“…The only reported postoperative complication is the disruption of the sutures at the lower end of the fistula; otherwise, if a coexisting biliary tree malformation is not recognized, the future of the involved hepatic segment is reported to be atrophy, abnormal bilious drainage, cholelithiasis, and late malignant degeneration. 7 A respiratory-biliary fistula must be considered in the differential diagnosis of a newborn child presenting with recurrent respiratory symptoms and bilious vomiting. After the diagnosis is made by bronchoscopy and/or HIDA scan, it is mandatory to look for associated biliary tree malformations.…”

“…Following the first report of this anomaly in 1952, only 18 cases have been described to date in the English literature. [2][3][4][5][6][7][8][9][10][11][12][13][14][15][16][17][18][19] We present two additional children who were identified in Italy (Table 1).…”