Congenital and Structural Abnormalities of the Liver

and, Ding-You Li; Schwarz, Kathleen B.

doi:10.1002/9780470987049.ch9

Cited by 1 publication

(2 citation statements)

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“…In all cases, accompanying liver findings include ductal plate malformation, fibrosis, and biliary cysts in different combinations [12]. …”

Section: Presinusoidal Portal Hypertensionmentioning

confidence: 99%

“…CHF has also been reported as part of other rare syndromes, such as nephronopthisis (with end-stage renal disease within 5 to 10 years), Jeune syndrome (lung and thoracic hypoplasia), Meckel-Gruber syndrome (encephalocele and polydactily), Ivemark syndrome (interstitial fibrosis leading to renal failure), chronic diarrhea related to enterocolitis cystic superficialis and intestinal lymphangiectasia, and others. In all cases, accompanying liver findings include ductal plate malformation, fibrosis, and biliary cysts in different combinations [ 12 ].…”

Section: Presinusoidal Portal Hypertensionmentioning

confidence: 99%

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Etiology and Management of Hemorrhagic Complications of Portal Hypertension in Children

Costaguta¹,

Álvarez

2012

International Journal of Hepatology

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Portal hypertension in children represents a particular diagnostic and management challenge for several reasons: (1) treatment outcomes should be evaluated in relationship with a long-life expectancy, (2) pediatric patients with portal hypertension constitute an heterogeneous population, both in terms of individual characteristics and diversity of liver diseases; making comparison between treatment outcomes very difficult, (3) application of techniques and procedures developed in adult patients (v.gr. TIPS) face size limitations in small children, and (4) absence of data from well-controlled trials in children forces pediatric specialists to adapt results obtained from adult cohorts suffering from diseases such as HCV and alcoholic cirrhosis. Despite those limitations, substantial progress in the treatment of children with portal hypertension has been achieved in recent years, with better outcomes and survival. Two main factors influence our therapeutic decision: age of the patient and etiology of the liver disease. Therefore, diagnosis and treatment of complications of portal hypertension in children need to be described taking such factors into consideration. This paper summarizes current knowledge and expert opinion.

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“…In all cases, accompanying liver findings include ductal plate malformation, fibrosis, and biliary cysts in different combinations [12]. …”

Section: Presinusoidal Portal Hypertensionmentioning

confidence: 99%

Section: Presinusoidal Portal Hypertensionmentioning

confidence: 99%