Congenital absence of the circumflex coronary artery associated with dilated cardiomyopathy

Bestetti, Reinaldo B.; Costa, Reynaldo B.; Oliveira, João Samuel Meira de; Rossi, Marcos A.; Araujo, Rosaly Corrêa de

doi:10.1016/0167-5273(85)90225-6

Cited by 8 publications

(6 citation statements)

References 2 publications

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“…There could be an association between the two conditions in patients with coronary artery hypoplasia (which could occur with an absent LCX and poorly developed RCA) that may give rise to myocardial fibrosis due to chronic ischaemia in the area of myocardial hypoperfusion and lead to a dilated cardiomyopathy. 12 However, in the case reported by Bestetti et al, 11 the pathological findings did not support any such association. In our patient too, cardiomyopathy also appears to be incidental, as myocardial perfusion imaging showed nil normal.…”

Section: Discussionmentioning

confidence: 81%

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Congenital Absence of Left Circumflex Coronary Artery: Role of Computed Tomography Coronary Angiography

Kapur¹,

Jain²,

Vashist³

2014

Hong Kong J Radiol

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Congenital coronary artery anomalies are infrequently seen during coronary angiography, and are usually diagnosed incidentally. Among such anomalies, absence of the left circumflex artery is extremely rare. We report on a 49-year-old man who presented with a 2-month history of increasing exertional breathlessness and was found to have poor left ventricular function on echocardiography. Routine coronary angiography showed a normal left anterior descending, no left circumflex artery and a dominant right coronary artery. Neither aortography nor pulmonary angiography showed a separate ostium for the left circumflex artery. Multidetector computed tomographic coronary angiography was performed to confirm the diagnosis of congenital absence of the left circumflex artery.

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Section: Discussionmentioning

confidence: 81%

“…In 1984, Bestetti et al 11 described the first autopsied case of congenital absence of the LCX in a 12-yearold girl clinically diagnosed as having idiopathic cardiomyopathy. The coexistence of the two conditions was postulated to be incidental.…”

Section: Discussionmentioning

confidence: 99%

Congenital Absence of Left Circumflex Coronary Artery: Role of Computed Tomography Coronary Angiography

Kapur¹,

Jain²,

Vashist³

2014

Hong Kong J Radiol

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“…It is difficult to explain the cause of restrictive cardiomyopathy seen in the patient under discussion. Although a hitherto undescribed causal relationship between isolated left circumflex coronary artery disease and restrictive cardiomyopathy can be suspected, the endomyocardial biopsy findings do not support this hypothesis [3,4]. Rather, they suggest that the restrictive cardiomyopathy may be a primary manifestation of Werner's syndrome, inasmuch as extensive fibrosis can be found in tissues other than the heart in this condition.…”

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confidence: 63%

Werner's syndrome and restrictive cardiomyopathy

Theodoropoulos¹,

Bestetti²,

Fonseca³

et al. 2006

International Journal of Cardiology

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“…Bestetti et al found absence of LCX with idiopathic dilated cardiomyopathy in autopsy [15]. These conditions may be accepted to co-exist by chance.…”

Section: Discussionmentioning

confidence: 99%

Absence of left circumflex coronary artery: and minireview

Ercan¹,

Sarı²,

Özer³

et al. 2012

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Absence of left circumflex coronary artery: case report and minireviewBrak gałęzi okalającej lewej tętnicy wieńcowej -opis przypadku i przegląd piśmiennictwa S Su ul le ey ym ma an n E Er rc ca an n 1 1 , , I Ib br ra ah hi im m S Sa ar ri i A b s t r a c tAbsence of the left circumflex coronary artery (LCX) is a very rare coronary anomaly. The anomaly has been reported in only 0.003% of all patients who underwent routine coronary angiography. Although rare, the failure to visualize a coronary artery in its expected anatomical location might cause life-threatening complications such as total occlusion with acute coronary syndromes. In the present paper, we report a patient with absent LCX and discuss the previously reported cases in terms of diagnostic and clinical importance, association with atherosclerosis and other anomalies. We searched Medline (www.ncbi.nlm.nih.gov) for cases of absent LCX and found that so far absence of LCX has been reported 27 times and in 32 cases. Here in this case report and minireview we discuss the characteristics of the present case and previous 32 cases with absence of LCX. The majority of the patients were over 30 years old at the time of diagnosis and the condition is more common in females. Although absence of LCX is generally considered as a benign entity, it might be atherosclerotic and can cause acute coronary syndromes including myocardial infarction and be associated with other anomalies. Proper diagnosis of the absence of LCX is very important because it can be misinterpreted as a totally occluded LCX. In subjects with absent LCX, infarction in the superdominant RCA might be more dangerous. It is more common in females and although conventional coronary angiography is the most widely used diagnostic modality, multidetector computed tomography might also be helpful. K Ke ey y w wo or rd ds s: : absent, left circumflex coronary artery

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Congenital absence of the circumflex coronary artery associated with dilated cardiomyopathy

Cited by 8 publications

References 2 publications

Congenital Absence of Left Circumflex Coronary Artery: Role of Computed Tomography Coronary Angiography

Congenital Absence of Left Circumflex Coronary Artery: Role of Computed Tomography Coronary Angiography

Werner's syndrome and restrictive cardiomyopathy

Absence of left circumflex coronary artery: and minireview

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