Congenital absence of pulmonary valve leaflets.

Buendı́a, Alfonso; Attié, Fause; Ovseyevitz, J; Zghaib, A; Zamora, C; Zavaleta, D; Vargas-Barrón, Jesús; Richheimer, Roberto

doi:10.1136/hrt.50.1.31

Cited by 14 publications

(3 citation statements)

References 36 publications

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“…The presence of incomplete right bundle branch block associated with right ventricular hypertrophy, as present in our case, can be of value in differentiating congenital APV from TOF. 4 Either pulmonary air entrapment with emphysema or atelectasis may result from the obstruction of the respective bronchus resulting from compression by the dilated pulmonary artery branches. Gross dilatation of the pulmonary artery and its branches with an abrupt transition in caliber between the main trunks and their immediate branches is typical of this malformation.…”

Section: Discussionmentioning

confidence: 99%

Absent Pulmonary Valve

Kariyappa

Agrawal

Srinivas

et al. 2014

World J Pediatr Congenit Heart Surg

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Congenital absence of the pulmonary valve is a rare congenital cardiac malformation, usually seen in association with tetralogy of Fallot. Patients generally present early in life with respiratory distress or recurrent respiratory tract infections, failure to thrive, cyanosis, infective endocarditis, or heart failure. Isolated absent pulmonary valve is quite rare and may be discovered in older age-group as in our patient, a nine-year-old male child who presented with atypical symptoms of exertional chest pain. Unusual echocardiographic features in this case include intact ventricular septum and prominent trabeculations of the right ventricle. Surgical implantation of a bioprosthetic valve was followed by hemodynamic and symptomatic improvement.

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Section: Discussionmentioning

confidence: 99%

Absent Pulmonary Valve

Kariyappa

Agrawal

Srinivas

et al. 2014

World J Pediatr Congenit Heart Surg

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“…Las radiografias de torax generalmente muestran cardiomegalia moderada, pero tambien han sido descritos casos con silueta cardiaca de tamano normal. La cardiomegalia ha sido relacionada con la severidad de la regurgitacion pulmonar 37 . La dilatacion de la arteria pulmonar se puede observar claramente en la proyeccion frontal, y la arteria pulmonar izquierda, puede identificarse mas facilmente en la proyeccion oblicua izquierda anterior.…”

Section: D1scusionunclassified

“…Esta rara malformacion cardiaca muy pocas veces se manifiesta como una lesion aislada: unicamente 6 casos han sido descritos 8 " 13 . Lo habitual es que se asocie a otras anomalies, mas frecuentemente tetralogi'a de Fallot 13 " 21 o CIV con o sin estenosis infundibular pulmonar, dando origen a un sindrome bastante caracterfstico 3 - 4 ' 13, 22-27 Hasta { a fecha 289 casos han sido publicados 13 -34 « 36 - 37 .…”

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Aplasia de las válvulas pulmonares

J²,

N³

et al. 1986

Rev. chil. pediatr.

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The clinical, phonocardiographic, hemodynamic and angiocaidiographic findings in 8 children with aplastic pulmonary valve are presented. All had a ventricular septal defect and in 6 there was aiso an infundibular pulmonic stenosis. Clinically, the most striking feature was late, low frecuency diastolic murmur of crecendo decrescendo quality and maximal intensity in the second and third left intercostal space, asociated with single, normal intensity second sound and, radiologically, abnormal parahiliar shadows, specially on the right side, or aneurysmatic dilatation of the pulmonary artery trunk. The angiocardiographic work-up usually showed aneurysmatic dilatation of the pulmonary artery trunk or his main branches and sudden peripheric reduction of their lumen. These findings are not seen in any other heart disease. The ethiology and results of surgical treatment of this abnormality are analized.

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Tetralogy of Fallot with “Absent” Pulmonary Valve

Freedom¹,

Rabinovitch²

1992

Neonatal Heart Disease

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Congenital absence of pulmonary valve leaflets.

Cited by 14 publications

References 36 publications

Absent Pulmonary Valve

Absent Pulmonary Valve

Aplasia de las válvulas pulmonares

Tetralogy of Fallot with “Absent” Pulmonary Valve

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