Congenital absence of coronary ostia in a single/common coronary system

Abstract

Coronary ostial atresia seen with pulmonary atresia and coronary-cameral fistulae or, more rarely, in isolation manifested as left main coronary artery atresia, is well described. We describe the clinical course and post-mortem findings in a neonate who suffered a fatal cardiac arrest and was found to have congenital absence of both coronary ostia in a single/common coronary system.

Atretic Coronary Artery Ostia in a Full-Term Infant with Early Postnatal Demise

“…To our knowledge, this is only the third case report published of this disease variant. 3,4 There are some similarities between the three cases as well as notable differences. As previously described in the case by Olabiyi et al, the entire coronary arterial system was only seen in communication with the RVOT.…”