Congenital Absence of a Pulmonary Artery: Its Demonstration by Roentgenography

Wyman, Stanley M.

doi:10.1148/62.3.321

Cited by 52 publications

(10 citation statements)

References 4 publications

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“…Congenital unilateral absence of a pulmonary artery is a rare anomaly that may occur in isolation but most frequently is accompanied by cardiovascular anomalies such as tetralogy of Fallot, right aortic arch, septal defects, patent ductus arteriosus [4,5,6], coarctation of an aorta [7], subvalvular aortic stenosis [8,] and transposition of great arteries [9]. …”

Section: Discussionmentioning

confidence: 99%

Congenital Absence of the Right Pulmonary Artery with Coronary Collaterals Supplying the Affected Lung: Effect on Coronary Perfusion

2007

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We describe a unique case of congenital absence of a right pulmonary artery presenting in a patient of advanced age and initially misdiagnosed as coronary artery disease. Perfusion of the affected lung was accomplished via anomalous collaterals from right and left circumflex coronary arteries which induced myocardial ischemia, as demonstrated by myocardial perfusion scan. To our knowledge there are only three reports in the international literature, describing unilateral pulmonary artery agenesis with the coronary artery supplying the abnormal lung. All these reports described that the existence of such vessels does not affect the myocardial perfusion. However, here we describe, to our knowledge, for the first time that in a patient with unilateral pulmonary artery agenesis, the existence of collaterals from the coronary arteries to the affected lung can actually have a negative effect in myocardial perfusion and can induce myocardial ischemia. In conclusion, clinicians should be aware of the possibility of undiagnosed cases of unilateral pulmonary artery agenesis presenting with chest pain in advanced age.

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Section: Discussionmentioning

confidence: 99%

Congenital Absence of the Right Pulmonary Artery with Coronary Collaterals Supplying the Affected Lung: Effect on Coronary Perfusion

2007

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“…It is a rare anomaly especially for adults, asymptomatic in 30% of patients or presented with mild symptoms at adulthood (1,2,3,4). Although generally left sided agenesis is presented with congenital cardiac malformations and right sided agenesis is usually isolated, our patient had isolated left sided pulmonary artery agenesis without other anomaly (2,5,6).…”

Section: Introductionmentioning

confidence: 99%

Isolated Left Pulmonary Artery Agenesis: A Case Report

Balcı

Koç²,

Kırkıl³

et al. 2012

MIRT

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Unilateral pulmonary artery agenesis without any cardiovascular malformation is a rare anomaly. We present the imaging findings of a patient who was diagnosed as isolated left pulmonary artery agenesis. A 27-year-old female patient was admitted to our hospital due to dyspnea during exercise for five years. Chest X-ray revealed minimally small left pulmonary hilum and left lung. She was admitted to our clinic with the suspicion of pulmonary artery pathology. Absent perfusion of the left lung with normal ventilation was visualized on scintigraphy. MDCT angiography of pulmonary arteries showed absent left main pulmonary artery with systemic collaterals around left hemithorax. Pulmonary artery agenesis can be asymptomatic and isolated until adulthood. Both scintigraphy and CT angiography images of pulmonary artery agenesis of a patient are rare in the literature. Pulmonary ventilation-perfusion scintigraphy can be used not only for pulmonary embolism but also pathologies involving pulmonary artery and its branches. Conflict of interest:None declared.

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“…Most of the other cases that have been reported have also been associated with a major cardiac or vascular defect, although Maier (1954) mentioned one in which no other anomaly could be found. Wyman (1954) likewise reported a case in which absence of the pulmonary artery was the sole defect, and Steinberg, Dotter, and Lukas (1953) described two others in patients aged 26 and 53 years. No associated congenital abnormalities in other systems have been cited.…”

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confidence: 95%

Absent Left Pulmonary Artery and Right-sided Aortic Arch in Eisenmenger's Complex

Fleming¹

1958

Thorax

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Congenital Absence of a Pulmonary Artery: Its Demonstration by Roentgenography

Cited by 52 publications

References 4 publications

Congenital Absence of the Right Pulmonary Artery with Coronary Collaterals Supplying the Affected Lung: Effect on Coronary Perfusion

Congenital Absence of the Right Pulmonary Artery with Coronary Collaterals Supplying the Affected Lung: Effect on Coronary Perfusion

Isolated Left Pulmonary Artery Agenesis: A Case Report

Absent Left Pulmonary Artery and Right-sided Aortic Arch in Eisenmenger's Complex

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