Conductive hearing loss: investigation of possible inner ear origin in three cases studies

Muhaimeed, Hamad Al; Sayed, Yousry El; Rabah, Abdulrahman; Al-Essa, Abdulrahman

doi:10.1258/00222150260369507

Cited by 11 publications

(3 citation statements)

References 11 publications

Supporting

Mentioning

Contrasting

Unclassified

Order By: Relevance

“…A hearing impairment with a consistent conductive element but without evidence of tympanic membrane or ossicular problems is termed inner-ear conductive hearing loss. 1,2 In 2003, two independent reports showed that dehiscence of bone overlying the superior semicircular canal (sSCC) can cause an inner-ear conductive hearing loss because of low-frequency bone conduction hearing gain and dissipation of air-conducted acoustic energy through the abnormal 'third window'. 3,4 Others have confirmed these findings, 5 and animal experiments support the third window hypothesis.…”

Section: Introductionmentioning

confidence: 99%

Mondini-like malformation mimicking otosclerosis and superior semicircular canal dehiscence

Karlberg¹,

Annertz

Magnusson³

2006

J. Laryngol. Otol.

View full text Add to dashboard Cite

In 2003, it was reported that superior semicircular canal dehiscence can mimic otosclerosis because of low-frequency bone conduction hearing gain and dissipation of air-conducted acoustic energy through the dehiscence. We report the case of a 17-year-old girl with left-sided combined hearing loss thought to be due to otosclerosis. Bone conduction thresholds were -10 dB at 250 and 500 Hz and she had a 40 dB air-bone gap at 250 Hz. When a tuning fork was placed at her ankle she heard it in her left ear. Acoustic reflexes and vestibular evoked myogenic potentials could be elicited bilaterally. Imaging of the temporal bones showed no otosclerosis, superior semicircular canal dehiscence or large vestibular aqueduct, but a left-sided, Mondini-like dysplasia of the cochlea with a modiolar deficiency could be seen. Mondini-like cochlear dysplasia should be added to the causes of inner-ear conductive hearing loss.

show abstract

Section: Introductionmentioning

confidence: 99%

Mondini-like malformation mimicking otosclerosis and superior semicircular canal dehiscence

Karlberg¹,

Annertz

Magnusson³

2006

J. Laryngol. Otol.

View full text Add to dashboard Cite

show abstract

“…exploratív tympanoto-ÖSSZEFOGLALÓ KÖZLEMÉNY mia, mely egyben terápiás lehetőséget is kínál. Időnként azonban a műtét során hiányoznak a halláscsökkenést megmagyarázó patológiai elváltozások a középfülben [1][2][3]. Az ilyen esetek hátterében a belső fül valamelyik struktúrájának olyan eltérése állhat, mely harmadik ablakként funkcionálva kivezeti a hangenergia egy részét a belső fülből [4][5][6][7].…”

unclassified

Harmadikablak-szindróma – osztályozás, diagnózis, terápia

Kalinics

Gerlinger

Révész

et al. 2020

View full text Add to dashboard Cite

Összefoglaló. Halláspanasszal számos beteg fordul orvoshoz. A rutinszerűen elvégzett súgottbeszéd-, hangvilla- és tisztahangküszöb-audiometriai vizsgálat alapján vezetéses, sensorineuralis, illetve a kettő együttes fennállása esetén kevert típusú halláscsökkenést különböztetünk meg. Vezetéses halláscsökkenés létrejöhet mind a külső, mind a közép- vagy a belső fül veleszületett vagy szerzett rendellenességei esetén. Amennyiben a stapediusreflex kiváltható, ugyanakkor a betegnél nincs jelen a külső fület, valamint a középfület érintő kórfolyamat, felmerül a harmadikablak-szindróma lehetősége. A kórkép okaként egy, a belső fül csontos tokján „harmadik ablakként” funkcionáló laesio van jelen, amely az ovális ablakon keresztül beérkező hangenergia egy részét elvezeti, mielőtt az a kerek ablakon át kivezetődik a középfülbe. A diagnózis felállítása gyakran nehéz feladat elé állítja a klinikust, melyhez a megfelelő audiológiai, illetve képalkotó vizsgálatok elvégzése elengedhetetlen. Tekintettel arra, hogy a panaszok megszüntetésére számos műtéti módszer került leírásra, közleményünkben átfogó képet adunk a kórkép etiológiájáról, diagnosztikájáról, terápiájáról, valamint bemutatjuk saját kezdeti tapasztalatainkat is 2 eset prezentálásával. Orv Hetil. 2020; 161(46): 1944–1952. Summary. Patients frequently present to the physician with hearing loss. Routine hearing tests include speech field (whisper test), tuning forks and pure tone threshold audiometry, which can identify the presence of sensorineural hearing loss, conductive hearing loss or a combination of both (mixed type). Conductive hearing loss can be a symptom of many different conditions. These include congenital or acquired malformations of the outer, middle and inner ear. If a conductive hearing loss with intact stapedial reflexes are recorded and in the absence of outer or middle ear pathology, then the third window syndrome should be considered. The cause is a bony defect on the otic capsule that acts as a ’third window’, dissipating the incoming sound energy. Without the appropriate audiological and imaging tests, the diagnosis of the condition is challenging in clinical setting. Several surgical techniques have been described to treat the condition. The authors give a comprehensive review of the etiology, diagnosis and treatment of the disease presenting their initial experiences with 2 cases. Orv Hetil. 2020; 161(46): 1944–1952.

show abstract

“…However, there have been reports of patients undergoing middle ear exploration with the intraoperative finding of a normal ossicular chain, despite a significant conductive hearing loss. 2,3 For many years, these patients were considered as having an “inner ear conductive hearing loss.” 4-6 More recently, it has been found that third window disorders, such as superior semicircular canal dehiscence and a dilated vestibular aqueduct, can also cause a conductive hearing loss, 7-9 and many patients with previously unclear causes of conductive hearing loss have been found to have such a third window disorder. 10-13 One potential way to avoid middle ear surgery in patients whose hearing loss is caused by a third window disorder is to obtain high-resolution computed tomography (CT) imaging of the temporal bone.…”

mentioning

confidence: 99%