Computed Tomography in Autosomal Dominant Polycystic Kidney Disease (Adpkd)

Abstract

ADPKD is the most common of the hereditary diseases (1:1000). It is a systemic hereditary disorder that is characterized by cyst formation in ductal organs, particularly the kidney and liver, gastrointestinal, cardiovascular and musculoskeletal abnormalities. 1 We present a case of a 55-year-old female with ADPKD. PKD is characterised by the presence of multiple cysts (Hence, "polycystic") typically in both kidneys; however, 17% of cases initially present with observable disease in one kidney with most cases progressing to bilateral disease in adulthood. 2 It is the most common hereditary cause of End-Stage Renal Failure (ESRF). 3 It accounts for 4-10% of all cases of ESRF. 3