Compulsive Repetitive Flexion With Breath-Holding in Sagging Brain Syndrome
Jeremy D. Schmahmann,
Wouter I. Schievink
Abstract:Background and ObjectiveSpontaneous intracranial hypotension (SIH) from CSF leak commonly produces headache. It also may produce sagging brain syndrome (SBS), often with neurocognitive symptoms indistinguishable from behavioral-variant frontotemporal dementia (bvFTD). The authors describe a new clinical sign that appears to be pathognomonic of SBS.
MethodsWe reviewed medical records and brain imaging in patients seen at our 2 centers who presented with SIH, SBS, and bvFTD symptoms.
ResultsThere were 51 patient… Show more
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