Complete penoscrotal transposition

Penoscrotal transposition and associated anomalies: Report of five new cases and review of the literature

“…Those described in the literature (Table IV) include complete atresia of the urinary system [Francis, 1940;Burkitt 1961;Miller, 19721, absence of one or both kidneys [Chappel, 1958;Remzi, 19661, horseshoe kidneys [Leb et al, 19741, ectopic pelvic kidney [Cohen-Addad et al, 1985;McKenzie et al, 19941, polycystic or dysplastic kidneys [Huffman, 1951;Anlar and Ayabakam, 1986;Lage et al, 1987;McKenzie et al, 19941, obstructive uropathy with reflux [Remzi, 1966;McKenzie et al, 19941, megaureter [Leb et al, 19741, and hydronephrosis [Cohen-Addad et al, 1985;Schofield et al, 1992;McKenzie et al, 19941. Mental retardation was observed in all 3 of our surviving cases (100%) and 3 of 7 survivors (43%) in the literature [Cohen-Addad et al, 1985;Remzi, 1966;Schofield et al, 19921. Hypospadias was observed in one of our cases (20%), and in 5/16 (31%) literature cases [Forshall and Rickham, 1956;Chappel, 1958;Leb et al, 1974;Cohen-Addad et al, 1985;Lage et al, 19871.…”

“…Mental retardation was observed in all 3 of our surviving cases (100%) and 3 of 7 survivors (43%) in the literature [Cohen-Addad et al, 1985;Remzi, 1966;Schofield et al, 19921. Hypospadias was observed in one of our cases (20%), and in 5/16 (31%) literature cases [Forshall and Rickham, 1956;Chappel, 1958;Leb et al, 1974;Cohen-Addad et al, 1985;Lage et al, 19871. Those patients with PST who did not have hypospadias manifested other urethral anomalies such as absence of penile urethra [Francis, 19401, diverticulum of prostatic urethra [McIlvoy and Harris, 19551, double urethra with two side-by-side slit-shaped urethral openings, both of which passed urine [Larsen, 19901 and hypoplastic urethra with meatal stenosis [McKenzie et al, 19941.…”

“…The clinical findings of the 5 cases are tabulated in Tables I, 11, and 111, and summarized along with 16 lit- [Francis, 1940;Huffman, 1951;McIlvoy and Harris, 1955;Forshall and Rickham, 1956;Chappel, 1958;Burkitt, 1961;Remzi, 1966;Miller, 1972;Leb et al, 1974;Paramo et al, 1981;Cohen-Addad et al, 1985;Anlar and Ayabakam, 1986;Lage et al, 1987;Larsen, 1990;Schofield et al, 1992;McKenzie et al, 19941. The remaining literature cases are not included in Table IV because of poor or no documentation of non-PST anomalies [Appelby, 1923;Hinman, 1935;Hontan, 1935;Gross, 1953;Guartieri and Segal, 1954;Campbell et al, 1963;Wilson et al, 1965;Nagata et al, 1966;Majumdar et al, 1968;Kapur and Krishnamurthy, 1968;Ghoneim and El Hamadi, 1971;Datta et al, 1971;Porteous et al, 19921.…”

Complete Penoscrotal Transposition: Case Report and Review of the Literature

“…We have identified 20 reported cases of complete PST in the literature since it was first recognized in 1923 (table 1) [6,7,8,9,10,11]. No concurrent major abnormality was reported in 3 of these cases, including 1 who underwent successful surgical correction [6,9].…”

Extreme penoscrotal transposition

“…[1,2] Less than 20 cases of extreme degree of PST with normal scrotum have been reported in the literature. [1][2][3][4][5][6][7] PST results from abnormal genital tubercle development around the 6th week gestation. It is associated with delay in the midline fusion of the urethral folds.…”