Comparative Study of Dentinogenesis Imperfecta in Different Families of the Same Topographical Region

Abstract

Dental hard tissue is subject to variety of disorders. Dentinogenesis Imperfecta is one such disorder attributed to heredity. It is known to be an autosomal dominant trait. Teeth with such ‘imperfect’ dentin are liable to be weak and discolored. The disease has variable penetration and therefore can be expressed as a range of phenotypic manifestations from mild discoloration and chipping to frank attrition and multiple pulp canal exposures. Here we present a comparative study of a series of cases from different families of one topographical region with widely different presentation and histories that are characteristic of this disease.

Osteogenesis imperfecta: potential therapeutic approaches

“…OI type V and VI do not seem to be affected by DI ( Schwartz & Tsipouras, 1984 ). The DI present in OI subjects is classified as Shields DI type I ( Shields, 1983 ) and is characterized by yellow to bluish-brown discoloration of teeth due to abnormal dentine ( Jindal et al, 2009 ; Shields, Bixler & El-Kafrawy, 1973 ) and short roots. Initially, the primary pulp chambers are uncharacteristically large, but they will calcify fairly rapidly.…”