Comment on “superficial siderosis of the central nervous system associated with ventral dural defects: bleeding from the epidural venous plexus”

Andereggen, Lukas; Steiger, Hans‐Jakob; Diepers, Michael; Marbacher, Serge

doi:10.1007/s00415-021-10654-y

Cited by 1 publication

(1 citation statement)

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“…These dural defects can be caused by cranio-spinal trauma occurring decades before presentation, by intervertebral disc microspurs [ 11 , 12 ], by connective tissue diseases that weaken the dura, or by spinal surgery [ 13 ]. The result is either that CSF slowly leaks out through the dural defect into the epidural space, causing the syndrome of SIH, or that blood from the ventral epidural venous plexus slowly leaks into the CSF and produces SS [ 14 , 15 ]. For reasons that are not yet clear, the two syndromes seldom coexist [ 16 ].…”

Section: Introductionmentioning

confidence: 99%

Progressive loss of hearing and balance in superficial siderosis due to occult spinal dural defects

Hálmagyi

Parker

Chen

et al. 2022

Eur Arch Otorhinolaryngol

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Purpose Superficial siderosis, a progressive, debilitating, neurological disease, often presents with bilateral impairment of auditory and vestibular function. We highlight that superficial siderosis is often due to a repairable spinal dural defect of the type that can also cause spontaneous intracranial hypotension. Methods Retrospective chart review of five patients presenting with moderate to severe, progressive bilateral sensorineural hearing loss as well as vestibular loss. All patients had developed superficial siderosis from spinal dural defects: three after trauma, one after spinal surgery and one from a thoracic discogenic microspur. Results The diagnosis was made late in all five patients; despite surgical repair in four, hearing and vestibular loss failed to improve. Conclusions In patients presenting with progressive bilateral sensorineural hearing loss, superficial siderosis should be considered as a possible cause. If these patients also have bilateral vestibular loss, cerebellar impairment and anosmia, then the diagnosis is likely and the inevitable disease progress might be halted by finding and repairing the spinal dural defect.

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