Combined general and epidural anesthesia for a child with alagille syndrome: a case report

Subramaniam, Kathirvel; Myers, Laura B.

doi:10.1111/j.1460-9592.2004.01285.x

Cited by 3 publications

(2 citation statements)

References 15 publications

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“…Although AGS regional anesthesia methods have been tried with success in some cases, bleeding disorders due to vitamin K deficiency is common in these patients. Therefore, caution should be exercised during regional anesthesia (6).…”

Section: Case Reportmentioning

confidence: 99%

Anaesthesia Management in Alagille Syndrome: A Case Report

Yıldırım¹,

Gümüş²,

Doğan³

et al. 2016

West Indian Med J

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Alagille syndrome (AGS) is one of the most common hereditary disorder that leads to chronic liver disease in children. It is an autosomal dominant disease. Frequency is 1/100 000. Jagged 1 gene mutation which causes microdeletion of twentieth chromosome can be detected in more than 90% of patients. As a result of examinations to a 3 years old patient admitted to our hospital due to dysuria, the patient is prepared for surgery since the results show bladder stone and ureter. Characteristic dysmorphic facial features, butterfly vertebrae, and posterior embriyotoxon as ocular findings were seen with patient. Hepatomegaly and splenomegaly were detected with physical examination and ultrasonography. Uretero cystoscopy and laser lithotripsy was performed to the patient undergoing general anesthesia. We emphasized that our experience in the anesthetic management of AGS is presented.

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Section: Case Reportmentioning

confidence: 99%

Anaesthesia Management in Alagille Syndrome: A Case Report

Yıldırım¹,

Gümüş²,

Doğan³

et al. 2016

West Indian Med J

View full text Add to dashboard Cite

show abstract

“…S ir —We would like to add to a recent report (1) concerning anesthesia for a child with Alagille syndrome. Our patient was a 5‐year‐old male child with Alagille syndrome who presented for dental rehabilitation.…”

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confidence: 99%