Clinical variants in Ebstein's anomaly

Tulino, Viviana; Cacace, Caterina; Tulino, Domenico; Imbalzano, Egidio; Dattilo, Giuseppe

doi:10.1016/j.ijcard.2013.07.138

Cited by 26 publications

(7 citation statements)

References 30 publications

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“…We have described a rare case of PAA with recurrent vessel dissection not susceptible to surgical correction in a patient with idiopathic PAH treated with triple oral specifi c therapy 7,8 and it highlights the diffi culties in managing these rare patients. Timing of eventual surgical repair of PAA is diffi cult to detect, especially when PAH drug therapy is effective, and the patient cannot be a candidate for lung transplantation.…”

Section: Discussionmentioning

confidence: 98%

Triple oral combination therapy in patients with idiopathic pulmonary arterial hypertension and recurrent vessel dissection of inoperable pulmonary artery aneurysm

Vatrano¹,

Orlando²,

Cassadonte³

et al. 2021

Cor Vasa

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Aneurysma na plicnici je vzácné postižení v důsledku zátěže cévní stěny při postupné dilataci. Jednoznačná defi nice a údaje o prevalenci tohoto postižení nejsou k dispozici. Plicní hypertenze je navíc život ohrožující a progredující postižení vyžadující specifi ckou léčbu. Kazuistika: Popisujeme případ 62leté bělošky s idiopatickou plicní hypertenzí a inoperabilním obrovským aneurysmatem na opakovaně disekované plicnici. Diagnóza byla stanovena snadno echokardiografi cky a výpočetní tomografi í. Obtížné bylo naopak rozhodování o léčbě, protože operatéři odmítli provést chirurgické odstranění aneurysmatu. Pacientku jsme léčili farmakologicky medikací specifi cky určenou pro plicní hypertenzi s cílem snížit tlak na plicnici. Diskuse: Popisujeme velmi vzácné a nesmírně závažné postižení charakterizované přítomností plicní hypertenze účinně léčené vhodnou perorální trojkombinací spolu s inoperabilním aneurysmatem na opakovaně disekované plicnici.

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Section: Discussionmentioning

confidence: 98%

Triple oral combination therapy in patients with idiopathic pulmonary arterial hypertension and recurrent vessel dissection of inoperable pulmonary artery aneurysm

Vatrano¹,

Orlando²,

Cassadonte³

et al. 2021

Cor Vasa

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“…Takotsubo syndrome (TS) is described as a pathology with a good prognosis characterized by the presence of a transient left ventricular wall disease without signifi cant culprit obstructive CAD. [1][2][3][4][5][6][7][8][9][10][11][12][13][14][15][16] The "golden standard" for a defi nitive diagnosis is invasive coronary angiography and ventriculography, with an integrated multi-imaging approach, such as echocardiography, fi rst--line non-invasive technique, and cardiac magnetic resonance (CMR), in order to discriminate TS from other acute cardiac syndromes with troponin elevation and ventricular disfunction. [16][17][18][19] Important hallmarks of TS are a relatively small increase in T/I troponin, the left ventricle "apical ballooning" (wall motion diskinesis characterized by apical akinesis and basal hyperkinesis) at echocardiography and ventriculography associated with normal epicardial coronary vessels at angiography.…”

Section: Introductionmentioning

confidence: 99%

Tako-tsubo syndrome and atrial fibrillation. New trigger for cardiomyopathy. A clinical case

Demurtas¹,

Sarro²,

Parato³

et al. 2022

Cor Vasa

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Takotsubo syndrom (TS) je znám i pod označením stresová kardiomyopatie. Spouštěči TS jsou vnější nebo vnitřní, fyzický nebo psychický stres spojený s katecholaminovou bouří, nadměrnou sympatickou aktivitou nervového systému nebo s dysfunkcí mikrovaskulatury v přítomnosti systémového zánětu. Popisujeme případ pacienta s takotsubo kardiomyopatií spojenou s fi brilací síní a s fi bromuskulární dysplazií levé přední sestupné větve.

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“…Some of their pathophysiological substrates are related to the electrophysiological properties of pluripotent stem cell-derived cardiomyocytes [5]. However the molecular, functional and morphological features of the myocardium are all involved in arrythmogenesis [6][7][8][9]. Atrial fibrillation and atrial flutter seem to be the less frequent, being almost always associated with specific and reversible conditions or to Fontan's surgical correction of univentricular heart or congenital heart diseases involving atrial dilatation [10].…”

Section: Introductionmentioning

confidence: 99%

Electroanatomical mapping systems and cardiac arrhythmias: avoiding radiations in pediatric patients

Casale¹,

Mezzetti²,

Tulino³

et al. 2017

J Neonatal Biol

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Introduction: Cardiac arrhythmias are challenging conditions in pediatric patients, especially in the case of newborns. Most of the tachyarrhythmias in children (90.24%) are atrioventricular reentrant tachycardias (AVRT) and atrioventricular nodal reentrant tachycardias (AVNRT). Although the standard 12-lead ECG maintains high diagnostic value, an invasive electrophysiological study with catheter ablation are often required. Unfortunately these procedures are burdened by the use of radiations. Materials and methods:We performed a systematic research in PubMed and Embase. We found 257 articles of interest but we selected only 36 as the most representative. Discussion:The main concerns linked to electrophysiological procedures are the need of fluoroscopy and thus the risk of malignancy as well as dermatitis, cataracts, thyroid diseases and birth defects in the patients' offspring. Children and especially newborns have a greater life expectancy so their cumulative risk is greater than adults. For this reason the guiding principle in electrophysiological procedures involving radiations in pediatric subjects is "as low as reasonably achievable" (acronym: ALARA). The development of 3-dimensional (3-D) electroanatomical mapping systems allowed a significant reduction of radiation exposure during catheter ablations. The most recent experiences demonstrated the feasibility and the safety of fluoroless ablation procedures of the most common arrhythmias in children.Conclusions: Cardiac arrhythmias could be very challenging conditions in pediatric patients. Predictors of complications are body weight <15 kg and age <4 years so it is clear that newborns are the most difficult patients. It is reasonable, because of these evidences, to approach cardiac arrhythmias pharmacologically in younger subjects. More than 20 years of experiences conducted by the electrophysiologists allow us to encourage the use of the electroanatomical mapping systems, with the objective of reducing the radiation exposure in children, especially when accessory pathways are involved. Citation: Casale M, Mezzetti M, Tulino V, Morelli M, Ciccarelli I, et al. (2017)

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Clinical variants in Ebstein's anomaly

Cited by 26 publications

References 30 publications

Triple oral combination therapy in patients with idiopathic pulmonary arterial hypertension and recurrent vessel dissection of inoperable pulmonary artery aneurysm

Triple oral combination therapy in patients with idiopathic pulmonary arterial hypertension and recurrent vessel dissection of inoperable pulmonary artery aneurysm

Tako-tsubo syndrome and atrial fibrillation. New trigger for cardiomyopathy. A clinical case

Electroanatomical mapping systems and cardiac arrhythmias: avoiding radiations in pediatric patients

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