Clinical presentation of rhabdomyoma of the heart in infancy and childhood

Surgery for Primary Cardiac Tumors in Children

“…[35][36][37][38] In our experience, incidence of tuberous sclerosis is consistently lower (47.0%) than what commonly reported (80%-90%). This is probably due to the surgical nature of this series.…”

Antenatal Ultrasound Diagnosis of Cardiac Rhabdomyoma in One of the Twins

“…The neoplastic nature of cardiac rhabdomyoma is controversial with many workers considering this to be a malformation [2]. Strong association between cardiac rhabdomyoma and tuberous sclerosis is consistent with this concept [3]. Cardiac rhabdomyoma was first described by Von Reckling Hausen in 1862 and occurs in about 50 percent of patients affected with tuberous sclerosis.…”

Primary Heart Tumors in Infancy and Childhood Report of Four Cases and Review of Literature

“…37) as well as intracavitarily right-(33) or left-sided (14). Rhabdomyomas often the cardiac manifestation of tuberous sclerosis -and rhabdomyosarcomas always develop intramurally in the beginning, later often protruding into the cavities and obstructing them (8,30).…”

“…Probably the tachyarrhyth mias are not based on a direct interference of the tumor with the conduction system, but rather on a re-entry mechanism by accessory, atrioventricular con duction bundles within the tumor (19). According to Sliaher et al (30), especial ly rhabdomyomas tend to tachyarrhythmias.…”

“…The consequences are lung congestion and passive pulmonary hypertension with the leading symptom of dyspnoea (see our case 4). Tumors of the left ven tricle cause the clinical and hemodynamic picture of a subaortic stenosis (30).…”