Clinical Experience With Infants With Robin Sequence: A Prospective Study

Marques, Inara; Sousa, Telma Vidotto de; Carneiro, Araken Fernando; Barbieri, Marco Antônio; Bettiol, Heloísa; Gutierrez, Manoel Romeu Pereira

doi:10.1597/1545-1569(2001)038<0171:cewiwr>2.0.co;2

Cited by 85 publications

(142 citation statements)

References 23 publications

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“…[4][5][6][7][8][9] The article concludes by proposing a single treatment protocol, which can be applied to all RS cases.…”

Section: Methodsmentioning

confidence: 99%

“…2,9 Type 1, which truly represents glossoptosis as the cause for airway obstruction, is the most frequent type observed in RS. 2,4,5 Studies carried out at HRAC-USP revealed that this type of obstruction occurs in 80% of the cases. 4,5 .…”

Section: Morphological and Genetic Aspectsmentioning

confidence: 97%

“…2,4,5 Studies carried out at HRAC-USP revealed that this type of obstruction occurs in 80% of the cases. 4,5 . The literature describes its best prognosis, in which 61% of the cases present with IRS.…”

Section: Morphological and Genetic Aspectsmentioning

confidence: 97%

“…8,20 The genetic syndrome that most frequently co-occurs with RS is Stickler syndrome, also known as hereditary arthroophthalmopathy. 4,5,21 In this syndrome, RS results from an intrinsic mandibular hypoplasia caused by poor penetration of the connective tissue through the palate. 22,23 A study conducted at HRAC-USP with 159 infants with RS reported the most frequent syndromes associated with this anomaly 4 (Table 1).…”

Section: Morphological and Genetic Aspectsmentioning

confidence: 99%

“…Several studies were conducted at the Hospital for Rehabilitation of Craniofacial Anomalies of Universidade de São Paulo (HRAC/USP) with the aim of resolving breathing and feeding difficulties in newborn infants, [4][5][6] which resulted in a different perspective of RS problems compared to most studies published in the international literature: RS is not only an anatomic obstructive disorder, but also a developmental disorder, and therefore it should be dealt with by a multidisciplinary team. Thus, the aim of the present article is to propose a single protocol for the treatment of breathing and feeding difficulties in newborns and infants with RS.…”

Section: Introductionmentioning

confidence: 99%

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Seqüência de Robin: protocolo único de tratamento

Marques¹,

Sousa²,

Carneiro³

et al. 2005

J. Pediatr. (Rio J.)

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Objective: To present a single protocol that might cover both the respiratory and feeding difficulties of neonates and infants with Robin sequence. Sources of data:The article was prepared on the basis of the most recent publications available in bibliographic databases and in books that discuss the treatment of Robin sequence, especially the studies conducted at the Hospital for Rehabilitation of Craniofacial Anomalies of Universidade de São Paulo (HRAC/USP). Summary of the findings:We present the morphological and genetic aspects of Robin sequence and concepts about nasopharyngoscopy and its clinical implications; we discuss the treatment of respiratory and feeding difficulties, and we present a single protocol for the treatment of all Robin sequence cases regardless of their severity and complexity.Conclusions: Robin sequence is not only an anatomic obstructive disorder to be treated with surgical procedures, but knowledge about childrens growth and development must be applied by a multidisciplinary team, since this permits the maintenance of airway permeability and of the ability to feed orally, often without the need of surgical procedures and their risks, especially when applied to neonates and small infants.

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“…[4][5][6][7][8][9] The article concludes by proposing a single treatment protocol, which can be applied to all RS cases.…”

Section: Methodsmentioning

confidence: 99%

Section: Morphological and Genetic Aspectsmentioning

confidence: 97%

Section: Morphological and Genetic Aspectsmentioning

confidence: 97%

Section: Morphological and Genetic Aspectsmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

See 3 more Smart Citations

Seqüência de Robin: protocolo único de tratamento

Marques¹,

Sousa²,

Carneiro³

et al. 2005

J. Pediatr. (Rio J.)

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Unravelling Robin sequence

Lieshout¹,

Joosten

Hoeve

et al. 2013

The Laryngoscope

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The prevalence of respiratory distress in children with Robin sequence is high. In most children, treatment with prone positioning was sufficient to relieve the airway obstruction. Successful treatment with prone positioning was significantly more often seen in children with an isolated Robin sequence. About one-third of all Robin sequence children needed respiratory support in the neonatal and/or infant period. However, in childhood, only 10% of the total Robin sequence cohort was still dependent on respiratory support.

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