Abstract:Background: Carriers of variations in the gene encoding bone morphogenetic protein receptor type 2 (BMPR2△) are at high risk for severe pulmonary arterial hypertension (PAH+).
Aim:To define the clinical and hemodynamic phenotype of BMPR2△/PAH+ patients.
Methods:We performed a systematic review encompassing observational data from January 2000 to July 2019 about BMPR2△ and confirmed PAH diagnosis. According to international clinical guidelines, we aimed to determine the clinical and hemodynamic phenotype of BMP… Show more
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