Ciliated hepatic foregut cysts in children

Zaydfudim, Victor M.; Rosen, Michael J.; Gillis, Lynette A.; Correa, Hernán; Lovvorn, Harold N.; Pinson, C. Wright; Kelly, Burnett S.

doi:10.1007/s00383-009-2468-x

Cited by 12 publications

(29 citation statements)

References 13 publications

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“…This cyst did not have cartilage but did have abundant mucous secreting glands and a ciliated epithelium. Other studies described mucous filled cysts lined with ciliated cells in the liver of infant [10][11][12], while others noted similar cysts in the retroperitoneum. To our knowledge, this is the first case report describing an intraabdominal bronchogenic cyst of the small bowel mesentery in the pediatric population.…”

Section: Discussionmentioning

confidence: 94%

Bronchogenic/Foregut Cyst of The Ileal Mesentery in a Child Mimicking Ovarian Mass

Markel

Lin

Fan

et al. 2013

Fetal and Pediatric Pathology

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Section: Discussionmentioning

confidence: 94%

Bronchogenic/Foregut Cyst of The Ileal Mesentery in a Child Mimicking Ovarian Mass

Markel

Lin

Fan

et al. 2013

Fetal and Pediatric Pathology

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“…Interestingly, our review of all pediatric cases revealed that approximately two thirds of the cysts in children were multilocular [2][3][4][5][6][7]11,13,15]. Three of our pediatric CHFCs were also multilocular.…”

Section: Discussionmentioning

confidence: 99%

“…Aggressive tumor behavior of SCC is demonstrated by the deaths of 2 of these patients within 2 and 9 months of tumor excision [2,11]. Previously, observation or aspiration of cysts has been recommended.…”

Section: Discussionmentioning

confidence: 99%

Ciliated Hepatic Foregut Cyst: Four Case Reports with a Review of the Literature

et al. 2011

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Ciliated hepatic foregut cysts (CHFCs) are rare congenital legions that arise from the embryonic foregut. The cysts are formed during fetal development by evagination from their respective portions of the foregut, and are characterized by a ciliated epithelial lining. Approximately 100 cases of CHFC have been reported, of which only 13 were in children. Although CHFC is typically benign, malignant transformation to squamous cell carcinoma (SCC) has been reported in 3 cases. Survival rate after progression to malignancy is poor, as SCC in this setting is biologically aggressive. We present 4 new cases of CHFC in children between 5 months and 17 years old. Our cases are unusual, as some of the cysts exhibit multilocularity and biliary communication, and 2 of our patients were diagnosed under the age of 1. Additionally, 1 of the cysts was 19.3 cm in diameter, making it the largest reported CHFC to our knowledge. Ciliated hepatic foregut cysts should be included in the differential diagnosis of hepatic lesions.

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“…Ele apresenta como característica típica a presença de quatro camadas da parede do cisto, distintas a microscopia. 8,9,10,11,12 A despeito de sua raridade, o CCH está aumentando em incidência. Este é sem dúvida devido ao aumento do uso de métodos de imagem radiológica não invasivos nos últimos 20 anos, acessibilidade e surgimento de novas técnicas de exames.…”

Section: Introductionunclassified

Cisto ciliado hepático: Revisão de Literatura

Santos

Levi²,

Côrtes³

et al. 2016

R. Saúde

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ResumoCisto ciliado hepático (CCH) é uma doença cística rara do fígado, acomete predominantemente homens adultos, geralmente assintomática. De origem embrionária do intestino anterior apresentam como características o tamanho médio de 3,6 cm, bem delimitados, uniloculares, localizados no segmento medial do lobo hepático esquerdo. O diagnóstico é baseado em achados incidentais de exames radiológicos com imagens hipoecóicas na ultrassonografia ,hipo ou isoatenuantes na tomografia computadorizada e hiperintensas na ponderação T2, na ressonância magnética. O diagnóstico definitivo é dado com o estudo histológico, evidenciando as quatro camadas típicas da parede do cisto. É importante o acompanhamento pela possibilidade de transformação maligna em torno de 5% dos casos. Este tema encontra sua relevância devido ao aumento de sua incidência, dificuldade de diagnóstico, complicações e a escassez de conhecimento da comunidade científica. O objetivo desta revisão de literatura é demonstrar a importância do diagnóstico, características clínico-diagnósticas e suspeita do quadro. Foi realizada uma revisão nas bases de dados eletrônicas no período de março de 2014 a julho de 2015. Os descritores utilizados foram: "cisto ciliado hepático", "diagnóstico de cisto ciliado hepático" e "imagem de cisto ciliado hepático". Enfatizamos a importância do CCH como diagnóstico diferencial para as lesões císticas do fígado, dado a sua importância para os pacientes sintomáticos com lesão e naqueles assintomáticos, devido ao risco de malignidade descrito pela literatura. A propedêutica complementar se faz necessária para elucidação do diagnóstico, sendo indispensável o estudo histopatológico. Palavras-Chave: Cisto ciliado hepático; Diagnóstico de cisto ciliado hepático; Imagem de cisto ciliado hepático. Ciliated hepatic foregut cyst (CHFC) is a rare cystic liver disease that predominantly affects adult men and is usually asymptomatic. From embryonic of the foregut origin, CHFC presents the average size of 3.6 cm and they are well defined, are unilocular and are located in the medial segment of the left hepatic lobe. Diagnosis is based on incidental finding in radiological examinations which are with hypoechoic images on ultrasound, hypo or isoattenuating on computer tomography and hyperintense on T2 ponderation on MRI. Definitive diagnosis is given with the histological study evidencing the four layers typical of the cyst wall. The monitoring is important because of the possibility of malignant transformation in about 5% of cases. This theme has relevance due to the increase in incidence, difficulty of diagnosis, complications and the lack of knowledge of the scientific community. The purpose of this literature review is to demonstrate the importance of the diagnosis, the clinical-diagnostic features and suspicion of the frame. A review was made on the period from March 2014 to July 2015. The descriptors used were: "ciliated hepatic foregut cyst"; "diagnosis of ciliated hepatic foregut cyst" and "image of ciliated hepatic foregut cyst". We e...

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Ciliated hepatic foregut cysts in children

Cited by 12 publications

References 13 publications

Bronchogenic/Foregut Cyst of The Ileal Mesentery in a Child Mimicking Ovarian Mass

Bronchogenic/Foregut Cyst of The Ileal Mesentery in a Child Mimicking Ovarian Mass

Ciliated Hepatic Foregut Cyst: Four Case Reports with a Review of the Literature

Cisto ciliado hepático: Revisão de Literatura

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