Abstract:La escoliosis distrófica de la neurofibromatosis se caracteriza por ser una cifoescoliosis de ángulo agudo que compromete un segmento corto de la columna vertebral y genera una gran deformidad que, sumada a los cambios distróficos de la columna, convierte a los gestos quirúrgicos para su corrección en verdaderos retos. Se presenta a un varón de 15 años con cifoescoliosis toracolumbar distrófica severa con ápice en T9, ángulo de Cobb 107° de escoliosis y 110,7° de cifosis segmentaria. Se realiza una cirugía por… Show more
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