Cicatricial upper and lower eyelid ectropion in an ichthyosis patient. Surgical correction.

Abstract

Background: Surgical correction of bilateral cicatricial upper and lower eyelid ectropion in an ichthyosis patient remains a challenge in clinical practice.Main observations: A 24-year-old female patient presented to our clinic with bilateral upper and lower eyelid ectropion. Her skin over her entire body and face was dry and scaly. The diagnosis was cicatricial ectropion related in a patient with ichthyosis. The upper eyelids were treated by retroauricular full thickness skin grafts and upper eyelid lateral tarsal strip procedure. And lower eyelids were treated by cheek transposition grafts and lower eyelid lateral tarsal strip procedure. The upper and lower eyelids were corrected successfully with these surgical procedures.Conclusions: In patients with ichthyosis skin alterations in the eyelid cause shortening of the anterior lamella, subsequently resulting with ectropion. Successful surgical correction with skin grafts or transposition flaps can be performed to lenghten anterior lamella. Adding lateral tarsal strip procedure to skin grafting helps to maintain a beter lid margin apposition. (J Dermatol Case Rep. 2011; 5(2): 27-29.) Cicatricial upper and lower eyelid ectropion in an ichthyosis patient. Surgical correction.

Ocular manifestations, complications and management of congenital ichthyoses: a new look

“…The use of cheek transposition flaps to correct lower eyelid ectropion have been reported in a single case of a 24-year old with LI and progressive ectropion along with postauricular grafts for upper eyelid ectropion 29. This is a useful method to introduce skin and lengthen the anterior lamella of the lower eyelid; however, applicability is limited as it requires a degree of facial skin laxity to recruit skin.…”

Topical Tazarotene for the Treatment of Ectropion in Ichthyosis

“…Many affected individuals cite ectropion as one of the most cosmetically displeasing aspects of their disease. There is currently no standard of care for the treatment of ectropion, and while surgical intervention is often attempted, 1-3 results are variable with frequent recurrence of ectropion or unsatisfactory cosmetic outcomes. 4,5 Recognizing that abnormal keratinization likely underlies ectropion, however, it is unsurprising that surgical intervention often fails.…”

Surgical management of the hand manifestations of Harlequin ichthyosis

“…The current body of literature on surgical management of Harlequin ichthyosis is small and focused largely on limb constriction/encasement or correction of the associated ectropion . The rarity of this disease makes its manifestations a challenge for any clinician who encounters it.…”

“…The current body of literature on surgical management of Harlequin ichthyosis is small and focused largely on limb constriction/ encasement 2,3 or correction of the associated ectropion. [4][5][6] The rarity of this disease makes its manifestations a challenge for any clinician who encounters it. The severe flexion contractures of the fingers, adduction contractures of the thumbs and pseudosyndactyly in this case were corrected using full-thickness skin grafting, with substantial improvement in both function and aesthetics of the hands.…”