Chorea Hyperglycaemia Basal Ganglia Syndrome in an Uncontrolled Diabetic Patient

Abstract

Chorea hyperglycaemia basal ganglia (CHBG) syndrome is a rare neurological manifestation that occurs in patients with uncontrolled type 2 diabetes, rarely can be manifested in type 1 diabetes as well. Also called as diabetic striatopathy (DS), it occurs in the background of non ketotic hyperglycaemia. DS predominantly leads to a unilateral reversible injury of the basal ganglia visualised as hyperintensities on MRI brain, resulting in various movement disorders such as hemichorea and hemiballismus. Being a rare yet reversible entity, its recognition and early treatment by the clinicians is important. Here, we report a case of 79 yr. old gentleman with CHBG syndrome, whose symptoms resolved with adequate glycaemic control. Keywords: Diabetes, Chorea, Hemiballismus