Chondrosarcome intracérébral frontal chez un enfant de 12 ans

Rationale:Extraskeletal myxoid chondrosarcoma (EMC) is a rare malignant neoplasm of which intracranial EMC is the rarest.Patient concerns:We present an unusual case report of a 41-year-old woman who was sent to the emergency department for a sudden headache and other symptoms related to increased intracranial pressure.Interventions:Emergent CT revealed an occupying lesion in the left cerebellum with surrounding edema. A complete surgical excision of the lesion through a transcortical approach was performed. After the operation, this patient received adjuvant radiotherapy and temozolomide treatment.Diagnoses:Pathology diagnosis was an intracranial EMC.Outcomes:The patient survives with no tumor recurrence as of the last follow-up. Progression-free survival exceeded 20 months.Lessons:We have reviewed the literature and here summarize the diagnosis and treatment options for intracranial EMC. Diagnosis and treatment options of this rare disease are discussed.

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“…Chondrosarcoma is a rare cartilaginous neoplasm, accounting for <0.5% of all intracranial neoplasms. [ 17 ]…”

Section: Review Of Literature and Discussionmentioning

confidence: 99%

Primary extraskeletal myxoid chondrosarcoma in cerebellum

Qin

Zhang

et al. 2017

Medicine

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“…[1][2][3][4][5][6][7][8][9][10][11][12][13][14][15][16][17]. Intracranial tumors of chondrosarcomatous origin represent less than 0.16% of all primary brain tumors[5].…”

mentioning

confidence: 99%

Metastatic Intracerebral Chondrosarcoma: Case Report and Literature Review of Endocrine Effects and Management Paradigms

Hussain

Ahmed

2020

Cureus

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The most common underlying diagnosis of intracranial tumor pathology is metastatic disease, followed by primary brain tumors. Chondrosarcomatous metastatic disease of the brain is a rare subtype of this disease process. The patient presented with right-sided weakness. Her history was significant for femur chondrosarcoma which was resected and treated. Laboratory analysis revealed persistent hypercalcemia and hyperglycemia. MRI of the brain was completed, which revealed a left parietal-occipital lesion with smaller lesions in the left frontal and right parietal lobe. Multidisciplinary tumor board recommended surgery for lesion resection and pathology. Surgical pathologic diagnosis after lesion resection was metastatic chondrosarcoma. The patient's preoperative arm and leg weakness improved after surgery. Our paper delineates this unique case of intracranial spread of femur chondrosarcoma.

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